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Acquired Hemophilia A in IgG4-Related Disease: Case Report, Immunopathogenic Study, and Review of the Literature

We report the observation of a 75-year-old patient referred for cervical lymphadenopathies. A pre-lymphadenectomy blood work revealed an asymptomatic elevation of aPTT with low factor VIII (FVIII) levels and high anti-FVIII antibodies titers, consistent with acquired hemophilia A (AHA). Histological...

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Detalles Bibliográficos
Autores principales:	Sanges, Sébastien, Jeanpierre, Emmanuelle, Lopez, Benjamin, Russick, Jules, Delignat, Sandrine, Carpentier, Benjamin, Dubois, Romain, Dubucquoi, Sylvain, Guerrier, Thomas, Hachulla, Éric, Hatron, Pierre-Yves, Paris, Camille, Susen, Sophie, Launay, David, Lacroix-Desmazes, Sébastien, Terriou, Louis
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2020
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7793697/ https://www.ncbi.nlm.nih.gov/pubmed/33424828 http://dx.doi.org/10.3389/fimmu.2020.558811

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