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Novel Therapeutic Approaches to Familial HLH (Emapalumab in FHL)

Primary Hemophagocytic lymphohistiocytosis (pHLH) is a rare, life-threatening, hyperinflammatory disorder, characterized by uncontrolled activation of the immune system. Mutations affecting several genes coding for proteins involved in the cytotoxicity machinery of both natural killer (NK) and T cel...

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Detalles Bibliográficos
Autores principales:	Merli, Pietro, Algeri, Mattia, Gaspari, Stefania, Locatelli, Franco
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2020
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7793976/ https://www.ncbi.nlm.nih.gov/pubmed/33424859 http://dx.doi.org/10.3389/fimmu.2020.608492

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