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Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a pa...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Wolters Kluwer - Medknow
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7810082/ https://www.ncbi.nlm.nih.gov/pubmed/33487709 http://dx.doi.org/10.4103/ijd.IJD_473_18 |
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author | Fernández, Iñigo Navarro Alonso, Susana Armesto Vian, Carlos Duran Cura, L Reguero Del González-Vela, Carmen González-López, Marcos |
author_facet | Fernández, Iñigo Navarro Alonso, Susana Armesto Vian, Carlos Duran Cura, L Reguero Del González-Vela, Carmen González-López, Marcos |
author_sort | Fernández, Iñigo Navarro |
collection | PubMed |
description | Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease. |
format | Online Article Text |
id | pubmed-7810082 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2020 |
publisher | Wolters Kluwer - Medknow |
record_format | MEDLINE/PubMed |
spelling | pubmed-78100822021-01-22 Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association Fernández, Iñigo Navarro Alonso, Susana Armesto Vian, Carlos Duran Cura, L Reguero Del González-Vela, Carmen González-López, Marcos Indian J Dermatol Case Report Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease. Wolters Kluwer - Medknow 2020 /pmc/articles/PMC7810082/ /pubmed/33487709 http://dx.doi.org/10.4103/ijd.IJD_473_18 Text en Copyright: © 2020 Indian Journal of Dermatology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms. |
spellingShingle | Case Report Fernández, Iñigo Navarro Alonso, Susana Armesto Vian, Carlos Duran Cura, L Reguero Del González-Vela, Carmen González-López, Marcos Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association |
title | Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association |
title_full | Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association |
title_fullStr | Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association |
title_full_unstemmed | Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association |
title_short | Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association |
title_sort | linear scleroderma and primary sclerosing cholangitis: an undescribed association |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7810082/ https://www.ncbi.nlm.nih.gov/pubmed/33487709 http://dx.doi.org/10.4103/ijd.IJD_473_18 |
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