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Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association

Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a pa...

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Autores principales: Fernández, Iñigo Navarro, Alonso, Susana Armesto, Vian, Carlos Duran, Cura, L Reguero Del, González-Vela, Carmen, González-López, Marcos
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7810082/
https://www.ncbi.nlm.nih.gov/pubmed/33487709
http://dx.doi.org/10.4103/ijd.IJD_473_18
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author Fernández, Iñigo Navarro
Alonso, Susana Armesto
Vian, Carlos Duran
Cura, L Reguero Del
González-Vela, Carmen
González-López, Marcos
author_facet Fernández, Iñigo Navarro
Alonso, Susana Armesto
Vian, Carlos Duran
Cura, L Reguero Del
González-Vela, Carmen
González-López, Marcos
author_sort Fernández, Iñigo Navarro
collection PubMed
description Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease.
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spelling pubmed-78100822021-01-22 Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association Fernández, Iñigo Navarro Alonso, Susana Armesto Vian, Carlos Duran Cura, L Reguero Del González-Vela, Carmen González-López, Marcos Indian J Dermatol Case Report Linear scleroderma (LS) is clinically characterized by the presence of sclerotic areas of skin, which develop in a linear pattern. Primary sclerosing cholangitis is a cholestatic disorder that can lead to end-stage liver disease. We present, for the first time in English literature, the case of a patient suffering from both the diseases. This highlights the fact that, even though LS has conventionally been considered to be a form of localized scleroderma, this does not necessarily imply that it is an exclusively cutaneous disease. Wolters Kluwer - Medknow 2020 /pmc/articles/PMC7810082/ /pubmed/33487709 http://dx.doi.org/10.4103/ijd.IJD_473_18 Text en Copyright: © 2020 Indian Journal of Dermatology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Fernández, Iñigo Navarro
Alonso, Susana Armesto
Vian, Carlos Duran
Cura, L Reguero Del
González-Vela, Carmen
González-López, Marcos
Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
title Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
title_full Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
title_fullStr Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
title_full_unstemmed Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
title_short Linear Scleroderma and Primary Sclerosing Cholangitis: An Undescribed Association
title_sort linear scleroderma and primary sclerosing cholangitis: an undescribed association
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7810082/
https://www.ncbi.nlm.nih.gov/pubmed/33487709
http://dx.doi.org/10.4103/ijd.IJD_473_18
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