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Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat

We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.

Detalles Bibliográficos
Autores principales: Van Meerhaeghe, Tess, Vandenbroucke, Frederik, Velkeniers, Brigitte
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7813405/
https://www.ncbi.nlm.nih.gov/pubmed/33462010
http://dx.doi.org/10.1136/bcr-2020-237331
Descripción
Sumario:We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.