Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat

We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.

Detalles Bibliográficos
Autores principales: Van Meerhaeghe, Tess, Vandenbroucke, Frederik, Velkeniers, Brigitte
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7813405/
https://www.ncbi.nlm.nih.gov/pubmed/33462010
http://dx.doi.org/10.1136/bcr-2020-237331
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author Van Meerhaeghe, Tess
Vandenbroucke, Frederik
Velkeniers, Brigitte
author_facet Van Meerhaeghe, Tess
Vandenbroucke, Frederik
Velkeniers, Brigitte
author_sort Van Meerhaeghe, Tess
collection PubMed
description We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated.
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spelling pubmed-78134052021-01-25 Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat Van Meerhaeghe, Tess Vandenbroucke, Frederik Velkeniers, Brigitte BMJ Case Rep Case Report We describe a case of a woman diagnosed at the age of 35 years with a generalised mediastinal and abdominal lymphangiomatosis associated with a protein losing enteropathy, who successfully improved when treatment with sirolimus was initiated. BMJ Publishing Group 2021-01-18 /pmc/articles/PMC7813405/ /pubmed/33462010 http://dx.doi.org/10.1136/bcr-2020-237331 Text en © BMJ Publishing Group Limited 2021. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ. http://creativecommons.org/licenses/by-nc/4.0/ http://creativecommons.org/licenses/by-nc/4.0/This is an open access article distributed in accordance with the Creative Commons Attribution Non Commercial (CC BY-NC 4.0) license, which permits others to distribute, remix, adapt, build upon this work non-commercially, and license their derivative works on different terms, provided the original work is properly cited and the use is non-commercial. See: http://creativecommons.org/licenses/by-nc/4.0/.
spellingShingle Case Report
Van Meerhaeghe, Tess
Vandenbroucke, Frederik
Velkeniers, Brigitte
Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
title Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
title_full Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
title_fullStr Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
title_full_unstemmed Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
title_short Systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
title_sort systemic generalised lymphangiomatosis: unknown aetiology and a challenge to treat
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7813405/
https://www.ncbi.nlm.nih.gov/pubmed/33462010
http://dx.doi.org/10.1136/bcr-2020-237331
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