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Genetic Restrictive Cardiomyopathy: Causes and Consequences—An Integrative Approach
The sarcomere as the smallest contractile unit is prone to alterations in its functional, structural and associated proteins. Sarcomeric dysfunction leads to heart failure or cardiomyopathies like hypertrophic (HCM) or restrictive cardiomyopathy (RCM) etc. Genetic based RCM, a very rare but severe d...
Autores principales: | Cimiotti, Diana, Budde, Heidi, Hassoun, Roua, Jaquet, Kornelia |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7827163/ https://www.ncbi.nlm.nih.gov/pubmed/33429969 http://dx.doi.org/10.3390/ijms22020558 |
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