Acyl-CoA thioesterase activity of peroxisomal ABC protein ABCD1 is required for the transport of very long-chain acyl-CoA into peroxisomes

The ABCD1 protein, one of the four ATP-binding cassette (ABC) proteins in subfamily D, is located on the peroxisomal membrane and is involved in the transport of very long chain fatty acid (VLCFA)-CoA into peroxisomes. Its mutation causes X-linked adrenoleukodystophy (X-ALD): an inborn error of pero...

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Detalles Bibliográficos
Autores principales: Kawaguchi, Kosuke, Mukai, Emi, Watanabe, Shiro, Yamashita, Atsushi, Morita, Masashi, So, Takanori, Imanaka, Tsuneo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group UK 2021
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7838297/
https://www.ncbi.nlm.nih.gov/pubmed/33500543
http://dx.doi.org/10.1038/s41598-021-81949-3

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