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ADAMTS13 and von Willebrand factor assessment in steady state and acute vaso‐occlusive crisis of sickle cell disease

BACKGROUND: Sickle cell disease (SCD) is characterized by vaso‐occlusive crisis (VOC), acute chest syndrome (ACS) and multiorgan failure (MOF) complicated by thrombosis. Von Willebrand factor (VWF) is a strong marker of SCD‐related endothelial injury. OBJECTIVES: To decipher the role of VWF and its...

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Detalles Bibliográficos
Autores principales:	Demagny, Julien, Driss, Aurélie, Stepanian, Alain, Anguel, Nadia, Affo, Louis, Roux, Damien, Habibi, Anoosha, Benghezal, Sandrine, Capdenat, Sophie, Coppo, Paul, Driss, Françoise, Veyradier, Agnès
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2020
Materias:	Original Articles ‐ Thrombosis
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7845082/ https://www.ncbi.nlm.nih.gov/pubmed/33537544 http://dx.doi.org/10.1002/rth2.12460

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