Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series

Hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome is an uncommon outcome of prolonged focal status epilepticus in childhood. We present four cases with age between 6 months and 3 years diagnosed with HHE syndrome. Two patients were lost to follow-up; other two cases had severe developmental delay an...

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Autores principales: Bhargava, Harshit, Dwivedi, Deepak
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7847093/
https://www.ncbi.nlm.nih.gov/pubmed/33531945
http://dx.doi.org/10.4103/jpn.JPN_27_19
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author Bhargava, Harshit
Dwivedi, Deepak
author_facet Bhargava, Harshit
Dwivedi, Deepak
author_sort Bhargava, Harshit
collection PubMed
description Hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome is an uncommon outcome of prolonged focal status epilepticus in childhood. We present four cases with age between 6 months and 3 years diagnosed with HHE syndrome. Two patients were lost to follow-up; other two cases had severe developmental delay and refractory epilepsy. An early diagnosis, a good seizure control, and a better understanding of the underlying mechanisms of HHE are needed to improve the outcome of this condition.
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spelling pubmed-78470932021-02-01 Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series Bhargava, Harshit Dwivedi, Deepak J Pediatr Neurosci Case Report Hemiconvulsion-hemiplegia-epilepsy (HHE) syndrome is an uncommon outcome of prolonged focal status epilepticus in childhood. We present four cases with age between 6 months and 3 years diagnosed with HHE syndrome. Two patients were lost to follow-up; other two cases had severe developmental delay and refractory epilepsy. An early diagnosis, a good seizure control, and a better understanding of the underlying mechanisms of HHE are needed to improve the outcome of this condition. Wolters Kluwer - Medknow 2020 2020-11-06 /pmc/articles/PMC7847093/ /pubmed/33531945 http://dx.doi.org/10.4103/jpn.JPN_27_19 Text en Copyright: © 2020 Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Bhargava, Harshit
Dwivedi, Deepak
Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series
title Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series
title_full Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series
title_fullStr Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series
title_full_unstemmed Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series
title_short Hemiconvulsion-hemiplegia-epilepsy Syndrome: A Case Series
title_sort hemiconvulsion-hemiplegia-epilepsy syndrome: a case series
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7847093/
https://www.ncbi.nlm.nih.gov/pubmed/33531945
http://dx.doi.org/10.4103/jpn.JPN_27_19
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