Cargando…

Mitochondrial Enzymes of the Urea Cycle Cluster at the Inner Mitochondrial Membrane

Mitochondrial enzymes involved in energy transformation are organized into multiprotein complexes that channel the reaction intermediates for efficient ATP production. Three of the mammalian urea cycle enzymes: N-acetylglutamate synthase (NAGS), carbamylphosphate synthetase 1 (CPS1), and ornithine t...

Descripción completa

Detalles Bibliográficos
Autores principales:	Haskins, Nantaporn, Bhuvanendran, Shivaprasad, Anselmi, Claudio, Gams, Anna, Kanholm, Tomas, Kocher, Kristen M., LoTempio, Jonathan, Krohmaly, Kylie I., Sohai, Danielle, Stearrett, Nathaniel, Bonner, Erin, Tuchman, Mendel, Morizono, Hiroki, Jaiswal, Jyoti K., Caldovic, Ljubica
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2021
Materias:	Physiology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7860981/ https://www.ncbi.nlm.nih.gov/pubmed/33551825 http://dx.doi.org/10.3389/fphys.2020.542950

Ejemplares similares

Inversion of allosteric effect of arginine on N-acetylglutamate synthase, a molecular marker for evolution of tetrapods
por: Haskins, Nantaporn, et al.
Publicado: (2008)

Expression Pattern and Biochemical Properties of Zebrafish N-Acetylglutamate Synthase
por: Caldovic, Ljubica, et al.
Publicado: (2014)

A novel bifunctional N-acetylglutamate synthase-kinase from Xanthomonas campestris that is closely related to mammalian N-acetylglutamate synthase
por: Qu, Qiuhao, et al.
Publicado: (2007)

Sources and Fates of Carbamyl Phosphate: A Labile Energy-Rich Molecule with Multiple Facets
por: Shi, Dashuang, et al.
Publicado: (2018)

Effect of arginine on oligomerization and stability of N-acetylglutamate synthase
por: Haskins, N., et al.
Publicado: (2016)

Gene delivery corrects N-acetylglutamate synthase deficiency and enables insights in the physiological impact of L-arginine activation of N-acetylglutamate synthase
por: Sonaimuthu, P., et al.
Publicado: (2021)

N-Acetylglutamate Synthase Deficiency Due to a Recurrent Sequence Variant in the N-acetylglutamate Synthase Enhancer Region
por: Williams, Monique, et al.
Publicado: (2018)

Transcriptional Regulation of N-Acetylglutamate Synthase
por: Heibel, Sandra Kirsch, et al.
Publicado: (2012)

NAGS, CPS1, and SLC25A13 (Citrin) at the Crossroads of Arginine and Pyrimidines Metabolism in Tumor Cells
por: Owusu-Ansah, Melissa, et al.
Publicado: (2023)

Paucity and Disparity of Publicly Available Sex-Disaggregated Data for the COVID-19 Epidemic Hamper Evidence-Based Decision-Making
por: Kocher, Kristen, et al.
Publicado: (2021)

A Novel N-Acetylglutamate Synthase Architecture Revealed by the Crystal Structure of the Bifunctional Enzyme from Maricaulis maris
por: Shi, Dashuang, et al.
Publicado: (2011)

Superresolution Imaging of Human Cytomegalovirus vMIA Localization in Sub-Mitochondrial Compartments
por: Bhuvanendran, Shivaprasad, et al.
Publicado: (2014)

Superresolution Imaging Identifies That Conventional Trafficking Pathways Are Not Essential for Endoplasmic Reticulum to Outer Mitochondrial Membrane Protein Transport
por: Salka, Kyle, et al.
Publicado: (2017)

N-acetylglutamate synthase deficiency: an insight into the genetics, epidemiology, pathophysiology, and treatment
por: Mew, Nicholas Ah, et al.
Publicado: (2011)

Urea cycle regulation by mitochondrial sirtuin, SIRT5
por: Nakagawa, Takashi, et al.
Publicado: (2009)

Urea Memory: Transient Cell Exposure to Urea Causes Persistent Mitochondrial ROS Production and Endothelial Dysfunction
por: d’Apolito, Maria, et al.
Publicado: (2018)

ISO 9000 in our company : self-study course for personnel
por: Kanholm, Jack
Publicado: (1994)

Unraveling the Peculiar Features of Mitochondrial Metabolism and Dynamics in Prostate Cancer
por: Fontana, Fabrizio, et al.
Publicado: (2023)

Mitochondrial hepatopathy: Anticipated difficulties in management of fatty acid oxidation defects and urea cycle defects
por: Ravindranath, Aathira, et al.
Publicado: (2022)

Promise and Pitfalls of Mitochondrial Replacement for Prevention and Cure of Heritable Neurodegenerative Diseases Caused by Deleterious Mutations in Mitochondrial DNA
por: Paine, Ananta, et al.
Publicado: (2016)

Transcription factor Ap2b regulates the mouse autosomal recessive polycystic kidney disease genes, Pkhd1 and Cys1
por: Wu, Maoqing, et al.
Publicado: (2023)

The N-Acetylglutamate Synthase Family: Structures, Function and Mechanisms
por: Shi, Dashuang, et al.
Publicado: (2015)

From Genome to Structure and Back Again: A Family Portrait of the Transcarbamylases
por: Shi, Dashuang, et al.
Publicado: (2015)

Annexin A1 Deficiency does not Affect Myofiber Repair but Delays Regeneration of Injured Muscles
por: Leikina, Evgenia, et al.
Publicado: (2015)

Membrane Stabilization by Modified Steroid Offers a Potential Therapy for Muscular Dystrophy Due to Dysferlin Deficit
por: Sreetama, Sen Chandra, et al.
Publicado: (2018)

Mitochondrial Membranes of Human SH-SY5Y Neuroblastoma Cells Express Serotonin 5-HT(7) Receptor
por: Tempio, Alessandra, et al.
Publicado: (2020)

Mitochondrial ATP synthase dimers spontaneously associate due to a long-range membrane-induced force
por: Anselmi, Claudio, et al.
Publicado: (2018)

Urea transport B gene induces melanoma B16 cell death via activation of p53 and mitochondrial apoptosis
por: Liu, Lianqin, et al.
Publicado: (2018)

Aryl urea substituted fatty acids: a new class of protonophoric mitochondrial uncoupler that utilises a synthetic anion transporter
por: Rawling, Tristan, et al.
Publicado: (2020)

Crystal Structure of the N-Acetyltransferase Domain of Human N-Acetyl-L-Glutamate Synthase in Complex with N-Acetyl-L-Glutamate Provides Insights into Its Catalytic and Regulatory Mechanisms
por: Zhao, Gengxiang, et al.
Publicado: (2013)

Baseline human gut microbiota profile in healthy people and standard reporting template
por: King, Charles H., et al.
Publicado: (2019)

Mitochondrial fragmentation enables localized signaling required for cell repair
por: Horn, Adam, et al.
Publicado: (2020)

Mitochondrial Dynamics in Mitochondrial Diseases
por: Suárez-Rivero, Juan M., et al.
Publicado: (2016)

“Development and Implementation of Novel Chatbot-based Genomic Research Consent”
por: Smith, Erica D., et al.
Publicado: (2023)

The Urine Microbiome of Healthy Men and Women Differs by Urine Collection Method
por: Pohl, Hans G., et al.
Publicado: (2020)

Impact of Cold Ischemia on Mitochondrial Function in Porcine Hearts and Blood Vessels
por: Wiedemann, Dominik, et al.
Publicado: (2013)

Mitochondrial dynamics and mitochondrial quality control
por: Ni, Hong-Min, et al.
Publicado: (2014)

The Mitochondrial Permeability Transition in Mitochondrial Disorders
por: Šileikytė, Justina, et al.
Publicado: (2019)

Calcium Trimetaphosphate-Loaded Electrospun Poly(Ester Urea) Nanofibers for Periodontal Tissue Engineering
por: Toledo, Priscila T. A., et al.
Publicado: (2023)

Molecular evolution of urea amidolyase and urea carboxylase in fungi
por: Strope, Pooja K, et al.
Publicado: (2011)

Cannot write session to /tmp/vufind_sessions/sess_shftpehi6g9umafga286esjvqp