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Clinical Validation of an Automated Fluorogenic Factor XIII Activity Assay Based on Isopeptidase Activity
Hereditary factor XIII (FXIII) deficiency is a rare autosomal bleeding disorder which can cause life-threatening bleeding. Acquired deficiency can be immune-mediated or due to increased consumption or reduced synthesis. The most commonly used screening test is insensitive, and widely used quantitati...
Autores principales: | Leitner, Martina, Büchold, Christian, Pasternack, Ralf, Binder, Nikolaus B., Moore, Gary W. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7863959/ https://www.ncbi.nlm.nih.gov/pubmed/33498248 http://dx.doi.org/10.3390/ijms22031002 |
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