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A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin

Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.

Detalles Bibliográficos
Autores principales: Sciumè, Mariarita, Serpenti, Fabio, Muratori, Simona, Pravettoni, Valerio, Ulivieri, Fabio Massimo, Croci, Giorgio Alberto, Migliorini, Anna Chiara, Esposito, Andrea, Goldaniga, Maria Cecilia, Saporiti, Giorgia Natascia, Galassi, Giulia, Baldini, Luca, Onida, Francesco, Grifoni, Federica Irene
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7869399/
https://www.ncbi.nlm.nih.gov/pubmed/33598282
http://dx.doi.org/10.1002/ccr3.3717
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author Sciumè, Mariarita
Serpenti, Fabio
Muratori, Simona
Pravettoni, Valerio
Ulivieri, Fabio Massimo
Croci, Giorgio Alberto
Migliorini, Anna Chiara
Esposito, Andrea
Goldaniga, Maria Cecilia
Saporiti, Giorgia Natascia
Galassi, Giulia
Baldini, Luca
Onida, Francesco
Grifoni, Federica Irene
author_facet Sciumè, Mariarita
Serpenti, Fabio
Muratori, Simona
Pravettoni, Valerio
Ulivieri, Fabio Massimo
Croci, Giorgio Alberto
Migliorini, Anna Chiara
Esposito, Andrea
Goldaniga, Maria Cecilia
Saporiti, Giorgia Natascia
Galassi, Giulia
Baldini, Luca
Onida, Francesco
Grifoni, Federica Irene
author_sort Sciumè, Mariarita
collection PubMed
description Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases.
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spelling pubmed-78693992021-02-16 A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin Sciumè, Mariarita Serpenti, Fabio Muratori, Simona Pravettoni, Valerio Ulivieri, Fabio Massimo Croci, Giorgio Alberto Migliorini, Anna Chiara Esposito, Andrea Goldaniga, Maria Cecilia Saporiti, Giorgia Natascia Galassi, Giulia Baldini, Luca Onida, Francesco Grifoni, Federica Irene Clin Case Rep Case Reports Management of systemic mastocytosis is an emerging challenge which requires a multidisciplinary diagnostic approach and personalized treatment strategy. Midostaurin can rapidly reduce the disease burden, also in cladribine refractory cases. John Wiley and Sons Inc. 2020-12-29 /pmc/articles/PMC7869399/ /pubmed/33598282 http://dx.doi.org/10.1002/ccr3.3717 Text en © 2020 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Reports
Sciumè, Mariarita
Serpenti, Fabio
Muratori, Simona
Pravettoni, Valerio
Ulivieri, Fabio Massimo
Croci, Giorgio Alberto
Migliorini, Anna Chiara
Esposito, Andrea
Goldaniga, Maria Cecilia
Saporiti, Giorgia Natascia
Galassi, Giulia
Baldini, Luca
Onida, Francesco
Grifoni, Federica Irene
A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
title A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
title_full A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
title_fullStr A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
title_full_unstemmed A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
title_short A case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
title_sort case of aggressive systemic mastocytosis with bulky lymphadenopathy showing response to midostaurin
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7869399/
https://www.ncbi.nlm.nih.gov/pubmed/33598282
http://dx.doi.org/10.1002/ccr3.3717
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