Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension

Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progre...

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Autores principales: Guimarães Rocha, Maria Sheila, Grangeiro Mirô, Hugo Salomão, Manfroi, Gregori, de Medeiros Dias, Arthur, Cardoso, Raphaella, Dozzi Brucki, Sonia Maria
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2021
Materias:
Single Case − General Neurology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7879318/
https://www.ncbi.nlm.nih.gov/pubmed/33613238
http://dx.doi.org/10.1159/000510847
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author Guimarães Rocha, Maria Sheila
Grangeiro Mirô, Hugo Salomão
Manfroi, Gregori
de Medeiros Dias, Arthur
Cardoso, Raphaella
Dozzi Brucki, Sonia Maria
author_facet Guimarães Rocha, Maria Sheila
Grangeiro Mirô, Hugo Salomão
Manfroi, Gregori
de Medeiros Dias, Arthur
Cardoso, Raphaella
Dozzi Brucki, Sonia Maria
author_sort Guimarães Rocha, Maria Sheila
collection PubMed
description Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs. Here we describe an atypical case of infratentorial SS evolving with acute intracranial hypertension in the absence of typical chronic signs.
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spelling pubmed-78793182021-02-18 Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension Guimarães Rocha, Maria Sheila Grangeiro Mirô, Hugo Salomão Manfroi, Gregori de Medeiros Dias, Arthur Cardoso, Raphaella Dozzi Brucki, Sonia Maria Case Rep Neurol Single Case − General Neurology Superficial siderosis (SS) of the nervous system is a rare acquired condition related to hemosiderin deposits in subpial layers of the brain, brainstem, cerebellum, cranial nerves, and spinal cord, leading to brain iron-mediated neurodegeneration. The cardinal neurological features are slowly progressive hearing loss, ataxia, and pyramidal signs. Here we describe an atypical case of infratentorial SS evolving with acute intracranial hypertension in the absence of typical chronic signs. S. Karger AG 2021-01-08 /pmc/articles/PMC7879318/ /pubmed/33613238 http://dx.doi.org/10.1159/000510847 Text en Copyright © 2021 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-4.0 International License (CC BY-NC) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Single Case − General Neurology
Guimarães Rocha, Maria Sheila
Grangeiro Mirô, Hugo Salomão
Manfroi, Gregori
de Medeiros Dias, Arthur
Cardoso, Raphaella
Dozzi Brucki, Sonia Maria
Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
title Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
title_full Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
title_fullStr Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
title_full_unstemmed Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
title_short Unusual Presentation in Infratentorial Superficial Siderosis: Acute Intracranial Hypertension
title_sort unusual presentation in infratentorial superficial siderosis: acute intracranial hypertension
topic Single Case − General Neurology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7879318/
https://www.ncbi.nlm.nih.gov/pubmed/33613238
http://dx.doi.org/10.1159/000510847
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