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Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor

INTRODUCTION: Extramedullary hemangioblastoma is a very rare entity that has been rarely reported in the literature. CASE PRESENTATION: A 17-year-old female presented with limping that rapidly progressed to paraparesis and urine incontinence over a one-month duration. Clinically, she had a small swe...

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Autores principales: Sereke, Senai Goitom, Bongomin, Felix, Owor, Geraldine
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7886093/
https://www.ncbi.nlm.nih.gov/pubmed/33603499
http://dx.doi.org/10.2147/IMCRJ.S294759
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author Sereke, Senai Goitom
Bongomin, Felix
Owor, Geraldine
author_facet Sereke, Senai Goitom
Bongomin, Felix
Owor, Geraldine
author_sort Sereke, Senai Goitom
collection PubMed
description INTRODUCTION: Extramedullary hemangioblastoma is a very rare entity that has been rarely reported in the literature. CASE PRESENTATION: A 17-year-old female presented with limping that rapidly progressed to paraparesis and urine incontinence over a one-month duration. Clinically, she had a small swelling on her spine. There was a diagnostic challenge when an enhanced magnetic resonance imaging (MRI) suggested dumbbell – shaped intradural extramedullary mass in the lower thoracic spine, hypointense on T1 and hyperintense on T2 sequences and heterointense on post contrast sequence. The radiologic differentials were pictures of nerve sheath tumors. However, histopathological examination of en bloc excisional biopsy showed hemangioblastoma with a differential of solitary fibrous tumor. Complete excision of the mass was done intraoperatively and the patient improved clinically. CONCLUSION: Contrast-enhanced MRI and histopathologic correlation are important for evaluating these rare tumors.
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spelling pubmed-78860932021-02-17 Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor Sereke, Senai Goitom Bongomin, Felix Owor, Geraldine Int Med Case Rep J Case Report INTRODUCTION: Extramedullary hemangioblastoma is a very rare entity that has been rarely reported in the literature. CASE PRESENTATION: A 17-year-old female presented with limping that rapidly progressed to paraparesis and urine incontinence over a one-month duration. Clinically, she had a small swelling on her spine. There was a diagnostic challenge when an enhanced magnetic resonance imaging (MRI) suggested dumbbell – shaped intradural extramedullary mass in the lower thoracic spine, hypointense on T1 and hyperintense on T2 sequences and heterointense on post contrast sequence. The radiologic differentials were pictures of nerve sheath tumors. However, histopathological examination of en bloc excisional biopsy showed hemangioblastoma with a differential of solitary fibrous tumor. Complete excision of the mass was done intraoperatively and the patient improved clinically. CONCLUSION: Contrast-enhanced MRI and histopathologic correlation are important for evaluating these rare tumors. Dove 2021-02-12 /pmc/articles/PMC7886093/ /pubmed/33603499 http://dx.doi.org/10.2147/IMCRJ.S294759 Text en © 2021 Sereke et al. http://creativecommons.org/licenses/by-nc/3.0/ This work is published and licensed by Dove Medical Press Limited. The full terms of this license are available at https://www.dovepress.com/terms.php and incorporate the Creative Commons Attribution – Non Commercial (unported, v3.0) License (http://creativecommons.org/licenses/by-nc/3.0/). By accessing the work you hereby accept the Terms. Non-commercial uses of the work are permitted without any further permission from Dove Medical Press Limited, provided the work is properly attributed. For permission for commercial use of this work, please see paragraphs 4.2 and 5 of our Terms (https://www.dovepress.com/terms.php).
spellingShingle Case Report
Sereke, Senai Goitom
Bongomin, Felix
Owor, Geraldine
Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
title Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
title_full Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
title_fullStr Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
title_full_unstemmed Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
title_short Dumbbell-Shaped Extramedullary Hemangioblastoma of the Thoracic Spine as a Diagnostic Dilemma of Solitary Fibrous Tumor
title_sort dumbbell-shaped extramedullary hemangioblastoma of the thoracic spine as a diagnostic dilemma of solitary fibrous tumor
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7886093/
https://www.ncbi.nlm.nih.gov/pubmed/33603499
http://dx.doi.org/10.2147/IMCRJ.S294759
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