Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series

Patients with restrictive cardiomyopathy due to Fabry disease are often deemed ineligible for left ventricular assist device (LVAD) support due to the risk of suction events with a small LV cavity. We describe the first case series of LVAD support for Fabry disease. LVAD therapy can improve survival...

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Detalles Bibliográficos
Autores principales: Omid Kiamanesh, M.D., Moayedi, Yasbanoo, Aleksova, Natasha, Posada, Juan Duero, Gershon, Ariel, Seidman, Michael A., Rao, Vivek, Billia, Filio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7893197/
https://www.ncbi.nlm.nih.gov/pubmed/33644734
http://dx.doi.org/10.1016/j.cjco.2020.09.024
Descripción
Sumario:Patients with restrictive cardiomyopathy due to Fabry disease are often deemed ineligible for left ventricular assist device (LVAD) support due to the risk of suction events with a small LV cavity. We describe the first case series of LVAD support for Fabry disease. LVAD therapy can improve survival, quality of life, and provide clinical stability to start enzyme replacement therapy. Precautions at the time of surgery include rapid treatment of fever to avoid Fabry crises, involvement of a multidisciplinary team, and early initiation of rehabilitation. We describe LVAD support for both bridging and destination therapy.

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