Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series

Patients with restrictive cardiomyopathy due to Fabry disease are often deemed ineligible for left ventricular assist device (LVAD) support due to the risk of suction events with a small LV cavity. We describe the first case series of LVAD support for Fabry disease. LVAD therapy can improve survival...

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Detalles Bibliográficos
Autores principales: Omid Kiamanesh, M.D., Moayedi, Yasbanoo, Aleksova, Natasha, Posada, Juan Duero, Gershon, Ariel, Seidman, Michael A., Rao, Vivek, Billia, Filio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7893197/
https://www.ncbi.nlm.nih.gov/pubmed/33644734
http://dx.doi.org/10.1016/j.cjco.2020.09.024
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author Omid Kiamanesh, M.D.
Moayedi, Yasbanoo
Aleksova, Natasha
Posada, Juan Duero
Gershon, Ariel
Seidman, Michael A.
Rao, Vivek
Billia, Filio
author_facet Omid Kiamanesh, M.D.
Moayedi, Yasbanoo
Aleksova, Natasha
Posada, Juan Duero
Gershon, Ariel
Seidman, Michael A.
Rao, Vivek
Billia, Filio
author_sort Omid Kiamanesh, M.D.
collection PubMed
description Patients with restrictive cardiomyopathy due to Fabry disease are often deemed ineligible for left ventricular assist device (LVAD) support due to the risk of suction events with a small LV cavity. We describe the first case series of LVAD support for Fabry disease. LVAD therapy can improve survival, quality of life, and provide clinical stability to start enzyme replacement therapy. Precautions at the time of surgery include rapid treatment of fever to avoid Fabry crises, involvement of a multidisciplinary team, and early initiation of rehabilitation. We describe LVAD support for both bridging and destination therapy.
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spelling pubmed-78931972021-02-25 Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series Omid Kiamanesh, M.D. Moayedi, Yasbanoo Aleksova, Natasha Posada, Juan Duero Gershon, Ariel Seidman, Michael A. Rao, Vivek Billia, Filio CJC Open Case Report Patients with restrictive cardiomyopathy due to Fabry disease are often deemed ineligible for left ventricular assist device (LVAD) support due to the risk of suction events with a small LV cavity. We describe the first case series of LVAD support for Fabry disease. LVAD therapy can improve survival, quality of life, and provide clinical stability to start enzyme replacement therapy. Precautions at the time of surgery include rapid treatment of fever to avoid Fabry crises, involvement of a multidisciplinary team, and early initiation of rehabilitation. We describe LVAD support for both bridging and destination therapy. Elsevier 2020-10-06 /pmc/articles/PMC7893197/ /pubmed/33644734 http://dx.doi.org/10.1016/j.cjco.2020.09.024 Text en © 2020 Canadian Cardiovascular Society. Published by Elsevier Inc. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Omid Kiamanesh, M.D.
Moayedi, Yasbanoo
Aleksova, Natasha
Posada, Juan Duero
Gershon, Ariel
Seidman, Michael A.
Rao, Vivek
Billia, Filio
Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series
title Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series
title_full Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series
title_fullStr Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series
title_full_unstemmed Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series
title_short Left Ventricular Assist Device Support for Fabry Cardiomyopathy: A Case Series
title_sort left ventricular assist device support for fabry cardiomyopathy: a case series
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7893197/
https://www.ncbi.nlm.nih.gov/pubmed/33644734
http://dx.doi.org/10.1016/j.cjco.2020.09.024
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