Cargando…

Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario

Congenital long QT syndrome (LQTS) is a rare cardiac condition characterized by abnormality of either sodium or potassium ion channels resulting in prolongation of QT interval and thereby predisposing to life-threatening arrhythmia. Once the syndrome is diagnosed, measures should be taken to avoid s...

Descripción completa

Detalles Bibliográficos
Autores principales: Raja, Javid, Menon, Sabarinath, Venkata, Devarakonda Bhargava, Unnikrishnan, KP, Namboodiri, Narayanan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7918017/
https://www.ncbi.nlm.nih.gov/pubmed/33679068
http://dx.doi.org/10.4103/apc.APC_146_19
_version_ 1783657831772192768
author Raja, Javid
Menon, Sabarinath
Venkata, Devarakonda Bhargava
Unnikrishnan, KP
Namboodiri, Narayanan
author_facet Raja, Javid
Menon, Sabarinath
Venkata, Devarakonda Bhargava
Unnikrishnan, KP
Namboodiri, Narayanan
author_sort Raja, Javid
collection PubMed
description Congenital long QT syndrome (LQTS) is a rare cardiac condition characterized by abnormality of either sodium or potassium ion channels resulting in prolongation of QT interval and thereby predisposing to life-threatening arrhythmia. Once the syndrome is diagnosed, measures should be taken to avoid sudden cardiac death. We present a rare case of LQTS associated with patent ductus arteriosus in a child, and a unique approach was used in managing both conditions.
format Online
Article
Text
id pubmed-7918017
institution National Center for Biotechnology Information
language English
publishDate 2021
publisher Wolters Kluwer - Medknow
record_format MEDLINE/PubMed
spelling pubmed-79180172021-03-05 Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario Raja, Javid Menon, Sabarinath Venkata, Devarakonda Bhargava Unnikrishnan, KP Namboodiri, Narayanan Ann Pediatr Cardiol Case Report Congenital long QT syndrome (LQTS) is a rare cardiac condition characterized by abnormality of either sodium or potassium ion channels resulting in prolongation of QT interval and thereby predisposing to life-threatening arrhythmia. Once the syndrome is diagnosed, measures should be taken to avoid sudden cardiac death. We present a rare case of LQTS associated with patent ductus arteriosus in a child, and a unique approach was used in managing both conditions. Wolters Kluwer - Medknow 2021 2020-09-23 /pmc/articles/PMC7918017/ /pubmed/33679068 http://dx.doi.org/10.4103/apc.APC_146_19 Text en Copyright: © 2020 Annals of Pediatric Cardiology http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Raja, Javid
Menon, Sabarinath
Venkata, Devarakonda Bhargava
Unnikrishnan, KP
Namboodiri, Narayanan
Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
title Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
title_full Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
title_fullStr Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
title_full_unstemmed Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
title_short Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
title_sort congenital long qt syndrome and patent ductus arteriosus: a rare surgical scenario
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7918017/
https://www.ncbi.nlm.nih.gov/pubmed/33679068
http://dx.doi.org/10.4103/apc.APC_146_19
work_keys_str_mv AT rajajavid congenitallongqtsyndromeandpatentductusarteriosusararesurgicalscenario
AT menonsabarinath congenitallongqtsyndromeandpatentductusarteriosusararesurgicalscenario
AT venkatadevarakondabhargava congenitallongqtsyndromeandpatentductusarteriosusararesurgicalscenario
AT unnikrishnankp congenitallongqtsyndromeandpatentductusarteriosusararesurgicalscenario
AT namboodirinarayanan congenitallongqtsyndromeandpatentductusarteriosusararesurgicalscenario