Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report

BACKGROUND: An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers–Danlos syndrome is a condition in which collagen production or its po...

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Autores principales: Starzyńska, Anna, Adamska, Paulina, Adamski, Łukasz, Sejda, Aleksandra, Wychowański, Piotr, Studniarek, Michał, Jereczek-Fossa, Barbara Alicja
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7941700/
https://www.ncbi.nlm.nih.gov/pubmed/33750365
http://dx.doi.org/10.1186/s12903-021-01472-9
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author Starzyńska, Anna
Adamska, Paulina
Adamski, Łukasz
Sejda, Aleksandra
Wychowański, Piotr
Studniarek, Michał
Jereczek-Fossa, Barbara Alicja
author_facet Starzyńska, Anna
Adamska, Paulina
Adamski, Łukasz
Sejda, Aleksandra
Wychowański, Piotr
Studniarek, Michał
Jereczek-Fossa, Barbara Alicja
author_sort Starzyńska, Anna
collection PubMed
description BACKGROUND: An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers–Danlos syndrome is a condition in which collagen production or its post-translational modifications are affected. Defects in connective tissues cause symptoms, which range from mild joint hypermobility to life-threatening complications. CASE PRESENTATION: We present an extremely rare case of an 11-year old girl with Ehlers–Danlos syndrome and coexistence of multiple odontogenic keratocysts. CONCLUSIONS: This case shows mainly atypical or rare association between multiple odontogenic keratocysts and Ehlers–Danlos syndrome.
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spelling pubmed-79417002021-03-09 Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report Starzyńska, Anna Adamska, Paulina Adamski, Łukasz Sejda, Aleksandra Wychowański, Piotr Studniarek, Michał Jereczek-Fossa, Barbara Alicja BMC Oral Health Case Report BACKGROUND: An odontogenic keratocyst is a lesion characterized by aggressive and infiltrative growth. The lesion is characterized by the existence of satellite microcysts (microtumours) and frequent recurrence (up to 30%). Ehlers–Danlos syndrome is a condition in which collagen production or its post-translational modifications are affected. Defects in connective tissues cause symptoms, which range from mild joint hypermobility to life-threatening complications. CASE PRESENTATION: We present an extremely rare case of an 11-year old girl with Ehlers–Danlos syndrome and coexistence of multiple odontogenic keratocysts. CONCLUSIONS: This case shows mainly atypical or rare association between multiple odontogenic keratocysts and Ehlers–Danlos syndrome. BioMed Central 2021-03-09 /pmc/articles/PMC7941700/ /pubmed/33750365 http://dx.doi.org/10.1186/s12903-021-01472-9 Text en © The Author(s) 2021 Open AccessThis article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated in a credit line to the data.
spellingShingle Case Report
Starzyńska, Anna
Adamska, Paulina
Adamski, Łukasz
Sejda, Aleksandra
Wychowański, Piotr
Studniarek, Michał
Jereczek-Fossa, Barbara Alicja
Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report
title Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report
title_full Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report
title_fullStr Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report
title_full_unstemmed Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report
title_short Multiple odontogenic keratocysts in Ehlers–Danlos syndrome: a rare case report
title_sort multiple odontogenic keratocysts in ehlers–danlos syndrome: a rare case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7941700/
https://www.ncbi.nlm.nih.gov/pubmed/33750365
http://dx.doi.org/10.1186/s12903-021-01472-9
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