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Giant Hepatomegaly with Spleno-testicular Enlargement in a Patient with Apolipoprotein A-I Amyloidosis: An Uncommon Type of Amyloidosis in Japan
Hereditary systemic amyloidosis aside from transthyretin-related familial amyloid polyneuropathy is quite uncommon in Japan. We herein report a sporadic case of hereditary apolipoprotein A-I (apoAI) amyloidosis. The patient was a 43-year-old Japanese man who exhibited marked hepatomegaly with spleno...
Autores principales: | Yoshinaga, Tsuneaki, Katoh, Nagaaki, Yazaki, Masahide, Sato, Mitsuto, Kametani, Fuyuki, Yasuda, Hideo, Watanabe, Kyohei, Kawata, Kazuhito, Nakagawa, Mayuko, Sekijima, Yoshiki |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Japanese Society of Internal Medicine
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7946490/ https://www.ncbi.nlm.nih.gov/pubmed/32999221 http://dx.doi.org/10.2169/internalmedicine.5126-20 |
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