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Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report

BACKGROUND: Darier–Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multipl...

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Detalles Bibliográficos
Autores principales: Triki, A., Aloui, M., Ghalleb, M., Jbir, I., Naceur, Ben, Hassouna, J. Ben, Chargui, R., Rahal, K.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7958428/
https://www.ncbi.nlm.nih.gov/pubmed/33715634
http://dx.doi.org/10.1186/s13256-021-02687-8
Descripción
Sumario:BACKGROUND: Darier–Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. CONCLUSION: DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.