Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report

BACKGROUND: Darier–Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multipl...

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Autores principales: Triki, A., Aloui, M., Ghalleb, M., Jbir, I., Naceur, Ben, Hassouna, J. Ben, Chargui, R., Rahal, K.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7958428/
https://www.ncbi.nlm.nih.gov/pubmed/33715634
http://dx.doi.org/10.1186/s13256-021-02687-8
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author Triki, A.
Aloui, M.
Ghalleb, M.
Jbir, I.
Naceur, Ben
Hassouna, J. Ben
Chargui, R.
Rahal, K.
author_facet Triki, A.
Aloui, M.
Ghalleb, M.
Jbir, I.
Naceur, Ben
Hassouna, J. Ben
Chargui, R.
Rahal, K.
author_sort Triki, A.
collection PubMed
description BACKGROUND: Darier–Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. CONCLUSION: DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
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spelling pubmed-79584282021-03-16 Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report Triki, A. Aloui, M. Ghalleb, M. Jbir, I. Naceur, Ben Hassouna, J. Ben Chargui, R. Rahal, K. J Med Case Rep Case Report BACKGROUND: Darier–Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. CASE PRESENTATION: A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. CONCLUSION: DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect. BioMed Central 2021-03-15 /pmc/articles/PMC7958428/ /pubmed/33715634 http://dx.doi.org/10.1186/s13256-021-02687-8 Text en © The Author(s) 2021 Open AccessThis article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated in a credit line to the data.
spellingShingle Case Report
Triki, A.
Aloui, M.
Ghalleb, M.
Jbir, I.
Naceur, Ben
Hassouna, J. Ben
Chargui, R.
Rahal, K.
Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
title Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
title_full Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
title_fullStr Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
title_full_unstemmed Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
title_short Giant Darier–Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
title_sort giant darier–ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7958428/
https://www.ncbi.nlm.nih.gov/pubmed/33715634
http://dx.doi.org/10.1186/s13256-021-02687-8
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