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Gender-Specific Effects of Two Treatment Strategies in a Mouse Model of Niemann-Pick Disease Type C1

In a mouse model of Niemann-Pick disease type C1 (NPC1), a combination therapy (COMBI) of miglustat (MIGLU), the neurosteroid allopregnanolone (ALLO) and the cyclic oligosaccharide 2-hydroxypropyl-β-cyclodextrin (HPßCD) has previously resulted in, among other things, significantly improved motor fun...

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Detalles Bibliográficos
Autores principales:	Holzmann, Carsten, Witt, Martin, Rolfs, Arndt, Antipova, Veronica, Wree, Andreas
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7962008/ https://www.ncbi.nlm.nih.gov/pubmed/33802605 http://dx.doi.org/10.3390/ijms22052539

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