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Periodontal Manifestation in a Patient with Kindler Syndrome

Kindler syndrome is a rare subtype of inherited epidermolysis bullosa. A 42-year-old female patient was admitted to our clinic with a complaint of tooth mobility. Multiple hypo- and hyperpigmented macules dissipated all over her body, prominent poikilodermatous changes, xerosis of the skin, and atro...

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Autores principales: Sari, Aysegul, Celik, Salih
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7963901/
https://www.ncbi.nlm.nih.gov/pubmed/33763263
http://dx.doi.org/10.1155/2021/6671229
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author Sari, Aysegul
Celik, Salih
author_facet Sari, Aysegul
Celik, Salih
author_sort Sari, Aysegul
collection PubMed
description Kindler syndrome is a rare subtype of inherited epidermolysis bullosa. A 42-year-old female patient was admitted to our clinic with a complaint of tooth mobility. Multiple hypo- and hyperpigmented macules dissipated all over her body, prominent poikilodermatous changes, xerosis of the skin, and atrophy were seen in the clinical extraoral examination. Intraoral examination showed atrophy of the buccal mucosa, limited oral opening, epidermal tissue easily separated from the connective tissue, painful ulcers of the hard palate, severe periodontitis, and keratosis of the lips. All of the teeth showed mobility. After dermatologist consultation, the diagnosis of the patient was clinically identified as “Kindler syndrome.” All of her teeth were extracted due to her progressive periodontal disease and late admission to our clinic. Periodontal treatment might be effective in treating and controlling oral symptoms related to the syndrome and in improving the patient's quality of life.
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spelling pubmed-79639012021-03-23 Periodontal Manifestation in a Patient with Kindler Syndrome Sari, Aysegul Celik, Salih Case Rep Dent Case Report Kindler syndrome is a rare subtype of inherited epidermolysis bullosa. A 42-year-old female patient was admitted to our clinic with a complaint of tooth mobility. Multiple hypo- and hyperpigmented macules dissipated all over her body, prominent poikilodermatous changes, xerosis of the skin, and atrophy were seen in the clinical extraoral examination. Intraoral examination showed atrophy of the buccal mucosa, limited oral opening, epidermal tissue easily separated from the connective tissue, painful ulcers of the hard palate, severe periodontitis, and keratosis of the lips. All of the teeth showed mobility. After dermatologist consultation, the diagnosis of the patient was clinically identified as “Kindler syndrome.” All of her teeth were extracted due to her progressive periodontal disease and late admission to our clinic. Periodontal treatment might be effective in treating and controlling oral symptoms related to the syndrome and in improving the patient's quality of life. Hindawi 2021-03-08 /pmc/articles/PMC7963901/ /pubmed/33763263 http://dx.doi.org/10.1155/2021/6671229 Text en Copyright © 2021 Aysegul Sari and Salih Celik. https://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Sari, Aysegul
Celik, Salih
Periodontal Manifestation in a Patient with Kindler Syndrome
title Periodontal Manifestation in a Patient with Kindler Syndrome
title_full Periodontal Manifestation in a Patient with Kindler Syndrome
title_fullStr Periodontal Manifestation in a Patient with Kindler Syndrome
title_full_unstemmed Periodontal Manifestation in a Patient with Kindler Syndrome
title_short Periodontal Manifestation in a Patient with Kindler Syndrome
title_sort periodontal manifestation in a patient with kindler syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7963901/
https://www.ncbi.nlm.nih.gov/pubmed/33763263
http://dx.doi.org/10.1155/2021/6671229
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