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Modifiers of CAG/CTG Repeat Instability: Insights from Mammalian Models

At fifteen different genomic locations, the expansion of a CAG/CTG repeat causes a neurodegenerative or neuromuscular disease, the most common being Huntington’s disease and myotonic dystrophy type 1. These disorders are characterized by germline and somatic instability of the causative CAG/CTG repe...

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Detalles Bibliográficos
Autores principales:	Wheeler, Vanessa C., Dion, Vincent
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	IOS Press 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7990408/ https://www.ncbi.nlm.nih.gov/pubmed/33579861 http://dx.doi.org/10.3233/JHD-200426

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