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Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma

Alveolar rhabdomyosarcoma (ARMS) arising in the corpus uteri is an extremely rare condition with exceptionally rapid progression and poor prognosis. Furthermore, ARMS is primarily diagnosed in the pediatric population. Due to rarity of the disease, there are no standard treatment guidelines. A 90-ye...

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Autores principales: Choi, Haewon, Lee, Hyunji, Kim, Hee Sun, Han, Jung Yeol, Chun, Kyoung-Chul
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Korean Society of Obstetrics and Gynecology 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7990999/
https://www.ncbi.nlm.nih.gov/pubmed/33631069
http://dx.doi.org/10.5468/ogs.20127
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author Choi, Haewon
Lee, Hyunji
Kim, Hee Sun
Han, Jung Yeol
Chun, Kyoung-Chul
author_facet Choi, Haewon
Lee, Hyunji
Kim, Hee Sun
Han, Jung Yeol
Chun, Kyoung-Chul
author_sort Choi, Haewon
collection PubMed
description Alveolar rhabdomyosarcoma (ARMS) arising in the corpus uteri is an extremely rare condition with exceptionally rapid progression and poor prognosis. Furthermore, ARMS is primarily diagnosed in the pediatric population. Due to rarity of the disease, there are no standard treatment guidelines. A 90-year-old woman was presented with a huge pelvic mass causing dyspnea and abdominal distension. The patient underwent debulking surgery and was diagnosed with uterine ARMS by fresh specimen biopsy. Despite intensive postoperative care, the patient died on the eighth postoperative day. Here, we report a case of uterine ARMS that will add to our understanding of this exceptionally rare type of tumor.
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spelling pubmed-79909992021-04-05 Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma Choi, Haewon Lee, Hyunji Kim, Hee Sun Han, Jung Yeol Chun, Kyoung-Chul Obstet Gynecol Sci Case Report Alveolar rhabdomyosarcoma (ARMS) arising in the corpus uteri is an extremely rare condition with exceptionally rapid progression and poor prognosis. Furthermore, ARMS is primarily diagnosed in the pediatric population. Due to rarity of the disease, there are no standard treatment guidelines. A 90-year-old woman was presented with a huge pelvic mass causing dyspnea and abdominal distension. The patient underwent debulking surgery and was diagnosed with uterine ARMS by fresh specimen biopsy. Despite intensive postoperative care, the patient died on the eighth postoperative day. Here, we report a case of uterine ARMS that will add to our understanding of this exceptionally rare type of tumor. Korean Society of Obstetrics and Gynecology 2021-03 2021-02-25 /pmc/articles/PMC7990999/ /pubmed/33631069 http://dx.doi.org/10.5468/ogs.20127 Text en Copyright © 2021 Korean Society of Obstetrics and Gynecology Articles published in Obstet Gynecol Sci are open-access, distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Choi, Haewon
Lee, Hyunji
Kim, Hee Sun
Han, Jung Yeol
Chun, Kyoung-Chul
Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
title Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
title_full Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
title_fullStr Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
title_full_unstemmed Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
title_short Uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
title_sort uterine alveolar rhabdomyosarcoma in an elderly patient manifesting extremely poor prognosis; a rare subtype of rhabdomyosarcoma
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7990999/
https://www.ncbi.nlm.nih.gov/pubmed/33631069
http://dx.doi.org/10.5468/ogs.20127
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