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Altered Expression of Peroxiredoxins in Mouse Model of Progressive Myoclonus Epilepsy upon LPS-Induced Neuroinflammation

Stefin B (cystatin B) is an inhibitor of endo-lysosomal cysteine cathepsin, and the loss-of-function mutations in the stefin B gene were reported in patients with Unverricht–Lundborg disease (EPM1), a form of progressive myoclonus epilepsy. Stefin B-deficient mice, a mouse model of the disease, disp...

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Detalles Bibliográficos
Autores principales:	Trstenjak Prebanda, Mojca, Matjan-Štefin, Petra, Turk, Boris, Kopitar-Jerala, Nataša
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7997206/ https://www.ncbi.nlm.nih.gov/pubmed/33673502 http://dx.doi.org/10.3390/antiox10030357

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