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Protein Substitute Requirements of Patients with Phenylketonuria on BH4 Treatment: A Systematic Review and Meta-Analysis

The traditional treatment for phenylketonuria (PKU) is a phenylalanine (Phe)-restricted diet, supplemented with a Phe-free/low-Phe protein substitute. Pharmaceutical treatment with synthetic tetrahydrobiopterin (BH4), an enzyme cofactor, allows a patient subgroup to relax their diet. However, dietar...

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Detalles Bibliográficos
Autores principales:	Ilgaz, Fatma, Marsaux, Cyril, Pinto, Alex, Singh, Rani, Rohde, Carmen, Karabulut, Erdem, Gökmen-Özel, Hülya, Kuhn, Mirjam, MacDonald, Anita
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8004763/ https://www.ncbi.nlm.nih.gov/pubmed/33807079 http://dx.doi.org/10.3390/nu13031040

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