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Arterial Wall Properties and Womersley Flow in Fabry Disease

BACKGROUND: Fabry disease is an X-linked recessive lysosomal storage disease resulting in the cellular accumulation of globotriaosylceramide particularly globotriaosylceramide. The disease is characterized by a dilated vasculopathy with arterial ectasia in muscular arteries and arterioles. Previous...

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Detalles Bibliográficos
Autores principales:	Moore, David F, Altarescu, Gheona, Pursley, Randall, Campia, Umberto, Panza, Julio A, Dimitriadis, Emilios, Schiffmann, Raphael
Formato:	Texto
Lenguaje:	English
Publicado:	BioMed Central 2002
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC80154/ https://www.ncbi.nlm.nih.gov/pubmed/11888483

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