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Anesthetic Management of a Child With Propionic Acidemia Complicated by Bacteremia and Severe Acute Respiratory Syndrome Coronavirus 2

Propionic acidemia (PA) is a rare, multi-systemic inborn error of metabolism. PA results from an impaired activity of the mitochondrial enzyme, propionyl-CoA carboxylase (PCC). PCC holds an essential role in the catabolic pathways for odd-chain fatty acids, cholesterol side-chains and branched-chain...

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Detalles Bibliográficos
Autores principales:	Sibulo, Lemuel, Kogel, William, Landolt, Luke, Seeni, Srikrishna, Markel, Jordan, Mlady, Andrew
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Elmer Press 2021
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8040449/ https://www.ncbi.nlm.nih.gov/pubmed/33984087 http://dx.doi.org/10.14740/jmc3628

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