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Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report
BACKGROUND: Salivary gland choristoma (SGCh) is a rare benign tumor reported in several unusual sites, such as the gastrointestinal tract, the optic nerve, and the internal auditory canal, but never reported in the inner ear. CASE PRESENTATION: An 8-year-old girl with a history of left profound cong...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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BioMed Central
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8051108/ https://www.ncbi.nlm.nih.gov/pubmed/33858521 http://dx.doi.org/10.1186/s40463-021-00511-3 |
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author | Yamanobe, Yoshiharu Oishi, Naoki Nishiyama, Takanori Hosoya, Makoto Ogawa, Kaoru |
author_facet | Yamanobe, Yoshiharu Oishi, Naoki Nishiyama, Takanori Hosoya, Makoto Ogawa, Kaoru |
author_sort | Yamanobe, Yoshiharu |
collection | PubMed |
description | BACKGROUND: Salivary gland choristoma (SGCh) is a rare benign tumor reported in several unusual sites, such as the gastrointestinal tract, the optic nerve, and the internal auditory canal, but never reported in the inner ear. CASE PRESENTATION: An 8-year-old girl with a history of left profound congenital hearing loss presented to us with ipsilateral progressive severe facial nerve palsy (House-Brackmann Grade VI). The left tympanic membrane was swollen with a pulsatile tumor. Radiological investigations revealed a multilocular tumor in the inner ear extending into the middle ear and internal auditory canal (IAC). We performed a partial resection of the tumor by transmastoid approach to preserve the anatomical structure of the facial nerve. The tumor was pathologically diagnosed as SGCh. Two years after surgery, her facial function recovered to House-Brackmann Grade II and the residual tumor did not show regrowth on MRI. CONCLUSIONS: Although the natural course of this rare tumor is unknown, a partial resection is an acceptable treatment procedure when functional recovery of the facial nerve is anticipated. GRAPHICAL ABSTRACT: [Image: see text] |
format | Online Article Text |
id | pubmed-8051108 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | BioMed Central |
record_format | MEDLINE/PubMed |
spelling | pubmed-80511082021-04-19 Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report Yamanobe, Yoshiharu Oishi, Naoki Nishiyama, Takanori Hosoya, Makoto Ogawa, Kaoru J Otolaryngol Head Neck Surg Case Report BACKGROUND: Salivary gland choristoma (SGCh) is a rare benign tumor reported in several unusual sites, such as the gastrointestinal tract, the optic nerve, and the internal auditory canal, but never reported in the inner ear. CASE PRESENTATION: An 8-year-old girl with a history of left profound congenital hearing loss presented to us with ipsilateral progressive severe facial nerve palsy (House-Brackmann Grade VI). The left tympanic membrane was swollen with a pulsatile tumor. Radiological investigations revealed a multilocular tumor in the inner ear extending into the middle ear and internal auditory canal (IAC). We performed a partial resection of the tumor by transmastoid approach to preserve the anatomical structure of the facial nerve. The tumor was pathologically diagnosed as SGCh. Two years after surgery, her facial function recovered to House-Brackmann Grade II and the residual tumor did not show regrowth on MRI. CONCLUSIONS: Although the natural course of this rare tumor is unknown, a partial resection is an acceptable treatment procedure when functional recovery of the facial nerve is anticipated. GRAPHICAL ABSTRACT: [Image: see text] BioMed Central 2021-04-15 /pmc/articles/PMC8051108/ /pubmed/33858521 http://dx.doi.org/10.1186/s40463-021-00511-3 Text en © The Author(s) 2021 https://creativecommons.org/licenses/by/4.0/Open AccessThis article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article's Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article's Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) . The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/ (https://creativecommons.org/publicdomain/zero/1.0/) ) applies to the data made available in this article, unless otherwise stated in a credit line to the data. |
spellingShingle | Case Report Yamanobe, Yoshiharu Oishi, Naoki Nishiyama, Takanori Hosoya, Makoto Ogawa, Kaoru Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
title | Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
title_full | Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
title_fullStr | Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
title_full_unstemmed | Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
title_short | Inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
title_sort | inner ear salivary gland choristoma extending to the middle ear with congenital profound hearing loss and facial palsy: a case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8051108/ https://www.ncbi.nlm.nih.gov/pubmed/33858521 http://dx.doi.org/10.1186/s40463-021-00511-3 |
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