Increased Alveolar Heparan Sulphate and Reduced Pulmonary Surfactant Amount and Function in the Mucopolysaccharidosis IIIA Mouse

Mucopolysaccharidosis IIIA (MPS IIIA) is a lysosomal storage disease with significant neurological and skeletal pathologies. Respiratory dysfunction is a secondary pathology contributing to mortality in MPS IIIA patients. Pulmonary surfactant is crucial to optimal lung function and has not been inve...

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Detalles Bibliográficos
Autores principales: Paget, Tamara L., Parkinson-Lawrence, Emma J., Trim, Paul J., Autilio, Chiara, Panchal, Madhuriben H., Koster, Grielof, Echaide, Mercedes, Snel, Marten F., Postle, Anthony D., Morrison, Janna L., Pérez-Gil, Jésus, Orgeig, Sandra
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8070179/
https://www.ncbi.nlm.nih.gov/pubmed/33918094
http://dx.doi.org/10.3390/cells10040849

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8070179/
https://www.ncbi.nlm.nih.gov/pubmed/33918094
http://dx.doi.org/10.3390/cells10040849

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