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Growth and Body Composition in PKU Children—A Three-Year Prospective Study Comparing the Effects of L-Amino Acid to Glycomacropeptide Protein Substitutes

Protein quality and quantity are important factors in determining lean body (muscle) mass (LBM). In phenylketonuria (PKU), protein substitutes provide most of the nitrogen, either as amino acids (AA) or glycomacropeptide with supplementary amino acids (CGMP-AA). Body composition and growth are impor...

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Detalles Bibliográficos
Autores principales:	Daly, Anne, Högler, Wolfgang, Crabtree, Nicola, Shaw, Nick, Evans, Sharon, Pinto, Alex, Jackson, Richard, Strauss, Boyd J., Wilcox, Gisela, Rocha, Júlio C., Ashmore, Catherine, MacDonald, Anita
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8073059/ https://www.ncbi.nlm.nih.gov/pubmed/33923714 http://dx.doi.org/10.3390/nu13041323

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