A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient

Dorsal pancreatic agenesis is a rare congenital pancreatic malformation. There is just 1 reported case associating it with choledochal cyst. However, no cases have reported yet with both coexisting with Hirschsprung disease. We report a case of a 23-year-old man, presenting with on and off epigastri...

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Autores principales: Chapa, Uday Kumar, Dutta, Souradeep, Remesh, Athul Minija, Jain, Ankit, Abhinaya, Reddy, Nelamangala Ramakrishnaiah, Vishnu Prasad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8078483/
https://www.ncbi.nlm.nih.gov/pubmed/33928176
http://dx.doi.org/10.14309/crj.0000000000000561
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author Chapa, Uday Kumar
Dutta, Souradeep
Remesh, Athul Minija
Jain, Ankit
Abhinaya, Reddy
Nelamangala Ramakrishnaiah, Vishnu Prasad
author_facet Chapa, Uday Kumar
Dutta, Souradeep
Remesh, Athul Minija
Jain, Ankit
Abhinaya, Reddy
Nelamangala Ramakrishnaiah, Vishnu Prasad
author_sort Chapa, Uday Kumar
collection PubMed
description Dorsal pancreatic agenesis is a rare congenital pancreatic malformation. There is just 1 reported case associating it with choledochal cyst. However, no cases have reported yet with both coexisting with Hirschsprung disease. We report a case of a 23-year-old man, presenting with on and off epigastric pain, sometimes radiating to the back. His medical records showed he had Hirschsprung disease as a neonate, for which he underwent Duhamel procedure. Ultrasound imaging revealed a choledochal cyst and a nonvisualized distal portion of the pancreas. Further cross-sectional imaging confirmed the findings—a type 1 choledochal cyst and a dorsal agenesis of the pancreas in a patient with Hirschsprung disease.
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spelling pubmed-80784832021-04-28 A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient Chapa, Uday Kumar Dutta, Souradeep Remesh, Athul Minija Jain, Ankit Abhinaya, Reddy Nelamangala Ramakrishnaiah, Vishnu Prasad ACG Case Rep J Case Report Dorsal pancreatic agenesis is a rare congenital pancreatic malformation. There is just 1 reported case associating it with choledochal cyst. However, no cases have reported yet with both coexisting with Hirschsprung disease. We report a case of a 23-year-old man, presenting with on and off epigastric pain, sometimes radiating to the back. His medical records showed he had Hirschsprung disease as a neonate, for which he underwent Duhamel procedure. Ultrasound imaging revealed a choledochal cyst and a nonvisualized distal portion of the pancreas. Further cross-sectional imaging confirmed the findings—a type 1 choledochal cyst and a dorsal agenesis of the pancreas in a patient with Hirschsprung disease. Wolters Kluwer 2021-04-26 /pmc/articles/PMC8078483/ /pubmed/33928176 http://dx.doi.org/10.14309/crj.0000000000000561 Text en © 2021 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (https://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Case Report
Chapa, Uday Kumar
Dutta, Souradeep
Remesh, Athul Minija
Jain, Ankit
Abhinaya, Reddy
Nelamangala Ramakrishnaiah, Vishnu Prasad
A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient
title A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient
title_full A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient
title_fullStr A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient
title_full_unstemmed A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient
title_short A Rare Case of Dorsal Agenesis of Pancreas, Choledochal Cyst, and Hirschsprung Disease in a Young Patient
title_sort rare case of dorsal agenesis of pancreas, choledochal cyst, and hirschsprung disease in a young patient
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8078483/
https://www.ncbi.nlm.nih.gov/pubmed/33928176
http://dx.doi.org/10.14309/crj.0000000000000561
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