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Familial Adenomatous Polyposis Associated With Bilateral Adrenocortical Tumors and Agressive Desmoid Tumor

Background: Familial adenomatous polyposis (FAP) is an autosomal dominant condition caused by germline mutation in the tumor suppressor gene APC. FAP occurs in 1 to 10.000 individuals, and is characterized by hundreds to thousands of colonic adenomatous polyps with a high risk of developing into col...

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Detalles Bibliográficos
Autores principales:	Neiva, Raíssa P, Santos, Larissa C O, Ledesma, Felipe L, Feher, Olavo, Srougi, Victor, Tanno, Fabio, Almeida, Madson Q, Chambo, Jose Luis, Mendonca, Berenice Bilharinho, Fragoso, Maria Candida
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Oxford University Press 2021
Materias:	Adrenal
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8090195/ http://dx.doi.org/10.1210/jendso/bvab048.266

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