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A Case of Peutz-Jeghers Syndrome Presenting With an Inoperable Periampullary Tumor

Peutz-Jeghers syndrome (PJS) is a syndrome characterized by multiple hamartomatous polyps in the gastrointestinal system and melanin pigments accumulating in the skin and mucous membranes. Patients with PJS have an increased risk of gastrointestinal malignancies. In this syndrome, pancreatic cancer...

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Detalles Bibliográficos
Autores principales: Ergenç, Muhammer, Uprak, Tevfik Kıvılcım
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8105654/
https://www.ncbi.nlm.nih.gov/pubmed/33972912
http://dx.doi.org/10.7759/cureus.14359
Descripción
Sumario:Peutz-Jeghers syndrome (PJS) is a syndrome characterized by multiple hamartomatous polyps in the gastrointestinal system and melanin pigments accumulating in the skin and mucous membranes. Patients with PJS have an increased risk of gastrointestinal malignancies. In this syndrome, pancreatic cancer is primarily detected in older ages. In this article, we present a case of a patient with an unresectable periampullary tumor and PJS.