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Lateral ventricular medulloepithelioma in children: a case report

Medulloepithelioma is an extremely rare highly malignant and rapidly growing tumor that occurs in the central nervous system. There are few reports of medulloepithelioma located in the ventricle. Medulloepithelioma is common in young children and adolescence. Herein, we described an unusual case of...

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Autores principales: You, Hong, Dong, Jiangtao, Xu, Jian, Zhao, Dong, Liu, Qi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: AME Publishing Company 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8107848/
https://www.ncbi.nlm.nih.gov/pubmed/34012850
http://dx.doi.org/10.21037/tp-20-257
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author You, Hong
Dong, Jiangtao
Xu, Jian
Zhao, Dong
Liu, Qi
author_facet You, Hong
Dong, Jiangtao
Xu, Jian
Zhao, Dong
Liu, Qi
author_sort You, Hong
collection PubMed
description Medulloepithelioma is an extremely rare highly malignant and rapidly growing tumor that occurs in the central nervous system. There are few reports of medulloepithelioma located in the ventricle. Medulloepithelioma is common in young children and adolescence. Herein, we described an unusual case of vomiting in a 4-year-old male patient with medulloepithelioma, presenting with enlarging head circumference. Because of computed tomography (CT) scan of the head showed signs of brain tumors and hydrocephalus, and enhanced magnetic resonance imaging (MRI) sequence showed increased heterogeneity and honeycomb-like changes on the mass after the administration of a contrast agent, the patient was first diagnosed as choroid plexus papilloma. After undergoing a surgical craniotomy, the patient was diagnosed as medulloepithelioma through pathological examination. We hope that this work will provide more understanding and knowledge of intracranial medulloepithelioma. For medulloepithelioma that occurs in the central nervous system, radiological examination is not sufficient to make a definite diagnosis of the tumor. Pathological examination can confirm the diagnosis of medulloepithelioma and distinguish it from other central system tumors. Surgical resection is a safe and effective method that can prolong the life of patients. However, the prognosis of medulloepithelioma is still poor, and further research is needed to improve the diagnosis and treatment of this rare disease.
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spelling pubmed-81078482021-05-18 Lateral ventricular medulloepithelioma in children: a case report You, Hong Dong, Jiangtao Xu, Jian Zhao, Dong Liu, Qi Transl Pediatr Case Report Medulloepithelioma is an extremely rare highly malignant and rapidly growing tumor that occurs in the central nervous system. There are few reports of medulloepithelioma located in the ventricle. Medulloepithelioma is common in young children and adolescence. Herein, we described an unusual case of vomiting in a 4-year-old male patient with medulloepithelioma, presenting with enlarging head circumference. Because of computed tomography (CT) scan of the head showed signs of brain tumors and hydrocephalus, and enhanced magnetic resonance imaging (MRI) sequence showed increased heterogeneity and honeycomb-like changes on the mass after the administration of a contrast agent, the patient was first diagnosed as choroid plexus papilloma. After undergoing a surgical craniotomy, the patient was diagnosed as medulloepithelioma through pathological examination. We hope that this work will provide more understanding and knowledge of intracranial medulloepithelioma. For medulloepithelioma that occurs in the central nervous system, radiological examination is not sufficient to make a definite diagnosis of the tumor. Pathological examination can confirm the diagnosis of medulloepithelioma and distinguish it from other central system tumors. Surgical resection is a safe and effective method that can prolong the life of patients. However, the prognosis of medulloepithelioma is still poor, and further research is needed to improve the diagnosis and treatment of this rare disease. AME Publishing Company 2021-04 /pmc/articles/PMC8107848/ /pubmed/34012850 http://dx.doi.org/10.21037/tp-20-257 Text en 2021 Translational Pediatrics. All rights reserved. https://creativecommons.org/licenses/by-nc-nd/4.0/Open Access Statement: This is an Open Access article distributed in accordance with the Creative Commons Attribution-NonCommercial-NoDerivs 4.0 International License (CC BY-NC-ND 4.0), which permits the non-commercial replication and distribution of the article with the strict proviso that no changes or edits are made and the original work is properly cited (including links to both the formal publication through the relevant DOI and the license). See: https://creativecommons.org/licenses/by-nc-nd/4.0 (https://creativecommons.org/licenses/by-nc-nd/4.0/) .
spellingShingle Case Report
You, Hong
Dong, Jiangtao
Xu, Jian
Zhao, Dong
Liu, Qi
Lateral ventricular medulloepithelioma in children: a case report
title Lateral ventricular medulloepithelioma in children: a case report
title_full Lateral ventricular medulloepithelioma in children: a case report
title_fullStr Lateral ventricular medulloepithelioma in children: a case report
title_full_unstemmed Lateral ventricular medulloepithelioma in children: a case report
title_short Lateral ventricular medulloepithelioma in children: a case report
title_sort lateral ventricular medulloepithelioma in children: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8107848/
https://www.ncbi.nlm.nih.gov/pubmed/34012850
http://dx.doi.org/10.21037/tp-20-257
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AT zhaodong lateralventricularmedulloepitheliomainchildrenacasereport
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