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A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult

Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported.

Detalles Bibliográficos
Autores principales: Rabadão, Tiago, Naia, Leonor, Ferreira, Filipa, Teixeira, Mariana, Aveiro, Marcelo, Eulálio, Margarida, Silva, Fernando
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8117811/
https://www.ncbi.nlm.nih.gov/pubmed/34026132
http://dx.doi.org/10.1002/ccr3.4006
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author Rabadão, Tiago
Naia, Leonor
Ferreira, Filipa
Teixeira, Mariana
Aveiro, Marcelo
Eulálio, Margarida
Silva, Fernando
author_facet Rabadão, Tiago
Naia, Leonor
Ferreira, Filipa
Teixeira, Mariana
Aveiro, Marcelo
Eulálio, Margarida
Silva, Fernando
author_sort Rabadão, Tiago
collection PubMed
description Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported.
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spelling pubmed-81178112021-05-20 A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult Rabadão, Tiago Naia, Leonor Ferreira, Filipa Teixeira, Mariana Aveiro, Marcelo Eulálio, Margarida Silva, Fernando Clin Case Rep Case Reports Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported. John Wiley and Sons Inc. 2021-03-28 /pmc/articles/PMC8117811/ /pubmed/34026132 http://dx.doi.org/10.1002/ccr3.4006 Text en © 2021 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Rabadão, Tiago
Naia, Leonor
Ferreira, Filipa
Teixeira, Mariana
Aveiro, Marcelo
Eulálio, Margarida
Silva, Fernando
A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
title A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
title_full A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
title_fullStr A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
title_full_unstemmed A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
title_short A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
title_sort case report of idiopathic hemophagocytic lymphohistiocytosis in an immunocompetent adult
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8117811/
https://www.ncbi.nlm.nih.gov/pubmed/34026132
http://dx.doi.org/10.1002/ccr3.4006
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