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A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult
Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported.
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8117811/ https://www.ncbi.nlm.nih.gov/pubmed/34026132 http://dx.doi.org/10.1002/ccr3.4006 |
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author | Rabadão, Tiago Naia, Leonor Ferreira, Filipa Teixeira, Mariana Aveiro, Marcelo Eulálio, Margarida Silva, Fernando |
author_facet | Rabadão, Tiago Naia, Leonor Ferreira, Filipa Teixeira, Mariana Aveiro, Marcelo Eulálio, Margarida Silva, Fernando |
author_sort | Rabadão, Tiago |
collection | PubMed |
description | Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported. |
format | Online Article Text |
id | pubmed-8117811 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | John Wiley and Sons Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-81178112021-05-20 A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult Rabadão, Tiago Naia, Leonor Ferreira, Filipa Teixeira, Mariana Aveiro, Marcelo Eulálio, Margarida Silva, Fernando Clin Case Rep Case Reports Hemophagocytic lymphohistiocytosis poses a diagnostic dilemma due to the absence of specific clinical and laboratory findings, especially in adults. Despite greater recognition of the disease, secondary idiopathic forms are still reported. John Wiley and Sons Inc. 2021-03-28 /pmc/articles/PMC8117811/ /pubmed/34026132 http://dx.doi.org/10.1002/ccr3.4006 Text en © 2021 The Authors. Clinical Case Reports published by John Wiley & Sons Ltd. https://creativecommons.org/licenses/by/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Reports Rabadão, Tiago Naia, Leonor Ferreira, Filipa Teixeira, Mariana Aveiro, Marcelo Eulálio, Margarida Silva, Fernando A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult |
title | A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult |
title_full | A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult |
title_fullStr | A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult |
title_full_unstemmed | A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult |
title_short | A case report of idiopathic Hemophagocytic lymphohistiocytosis in an immunocompetent adult |
title_sort | case report of idiopathic hemophagocytic lymphohistiocytosis in an immunocompetent adult |
topic | Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8117811/ https://www.ncbi.nlm.nih.gov/pubmed/34026132 http://dx.doi.org/10.1002/ccr3.4006 |
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