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Anesthetic Management for Pediatric Liver Transplantation in a Patient With Propionic Acidemia: A Case Report

Propionic acidemia is an inborn error of metabolism characterized by accumulation of propionic acid due to deficiency of propionyl-CoA carboxylase. Main stay of treatment focuses on reducing dietary protein. However, orthotropic liver transplantation decreases the frequency of metabolic decompensati...

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Detalles Bibliográficos
Autores principales:	Rodriguez, Luis I., Tainsh, Erica J., Varga, Eliane, Mavarez, Ana C.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	SAGE Publications 2021
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8120524/ https://www.ncbi.nlm.nih.gov/pubmed/33978500 http://dx.doi.org/10.1177/23247096211015025

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