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Multisystem Langerhans Cell Histiocytosis in an infant
Langerhans cell histiocytosis (LCH) is a rare enigmatic disease that pre-dominantly affects children under 5 years of age. We report an interesting case of a 5 month old female diagnosed with multisystem LCH. Her disease process included osseous, pulmonary, gastrointestinal, cutaneous, hematopoietic...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8120863/ https://www.ncbi.nlm.nih.gov/pubmed/34025890 http://dx.doi.org/10.1016/j.radcr.2021.04.028 |
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author | Ji, William Ladner, Joshua Rambie, Aimee Boyer, Kathleen |
author_facet | Ji, William Ladner, Joshua Rambie, Aimee Boyer, Kathleen |
author_sort | Ji, William |
collection | PubMed |
description | Langerhans cell histiocytosis (LCH) is a rare enigmatic disease that pre-dominantly affects children under 5 years of age. We report an interesting case of a 5 month old female diagnosed with multisystem LCH. Her disease process included osseous, pulmonary, gastrointestinal, cutaneous, hematopoietic and neurologic involvement. This case highlights the varying clinical symptoms, risk factors, pathogenesis, and management of multisystem LCH. This case also emphasizes the role of diagnostic imaging in this multifaceted disease. |
format | Online Article Text |
id | pubmed-8120863 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-81208632021-05-20 Multisystem Langerhans Cell Histiocytosis in an infant Ji, William Ladner, Joshua Rambie, Aimee Boyer, Kathleen Radiol Case Rep Case Report Langerhans cell histiocytosis (LCH) is a rare enigmatic disease that pre-dominantly affects children under 5 years of age. We report an interesting case of a 5 month old female diagnosed with multisystem LCH. Her disease process included osseous, pulmonary, gastrointestinal, cutaneous, hematopoietic and neurologic involvement. This case highlights the varying clinical symptoms, risk factors, pathogenesis, and management of multisystem LCH. This case also emphasizes the role of diagnostic imaging in this multifaceted disease. Elsevier 2021-05-06 /pmc/articles/PMC8120863/ /pubmed/34025890 http://dx.doi.org/10.1016/j.radcr.2021.04.028 Text en © 2021 Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Ji, William Ladner, Joshua Rambie, Aimee Boyer, Kathleen Multisystem Langerhans Cell Histiocytosis in an infant |
title | Multisystem Langerhans Cell Histiocytosis in an infant |
title_full | Multisystem Langerhans Cell Histiocytosis in an infant |
title_fullStr | Multisystem Langerhans Cell Histiocytosis in an infant |
title_full_unstemmed | Multisystem Langerhans Cell Histiocytosis in an infant |
title_short | Multisystem Langerhans Cell Histiocytosis in an infant |
title_sort | multisystem langerhans cell histiocytosis in an infant |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8120863/ https://www.ncbi.nlm.nih.gov/pubmed/34025890 http://dx.doi.org/10.1016/j.radcr.2021.04.028 |
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