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Multisystem Langerhans Cell Histiocytosis in an infant

Langerhans cell histiocytosis (LCH) is a rare enigmatic disease that pre-dominantly affects children under 5 years of age. We report an interesting case of a 5 month old female diagnosed with multisystem LCH. Her disease process included osseous, pulmonary, gastrointestinal, cutaneous, hematopoietic...

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Detalles Bibliográficos
Autores principales: Ji, William, Ladner, Joshua, Rambie, Aimee, Boyer, Kathleen
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8120863/
https://www.ncbi.nlm.nih.gov/pubmed/34025890
http://dx.doi.org/10.1016/j.radcr.2021.04.028
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author Ji, William
Ladner, Joshua
Rambie, Aimee
Boyer, Kathleen
author_facet Ji, William
Ladner, Joshua
Rambie, Aimee
Boyer, Kathleen
author_sort Ji, William
collection PubMed
description Langerhans cell histiocytosis (LCH) is a rare enigmatic disease that pre-dominantly affects children under 5 years of age. We report an interesting case of a 5 month old female diagnosed with multisystem LCH. Her disease process included osseous, pulmonary, gastrointestinal, cutaneous, hematopoietic and neurologic involvement. This case highlights the varying clinical symptoms, risk factors, pathogenesis, and management of multisystem LCH. This case also emphasizes the role of diagnostic imaging in this multifaceted disease.
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spelling pubmed-81208632021-05-20 Multisystem Langerhans Cell Histiocytosis in an infant Ji, William Ladner, Joshua Rambie, Aimee Boyer, Kathleen Radiol Case Rep Case Report Langerhans cell histiocytosis (LCH) is a rare enigmatic disease that pre-dominantly affects children under 5 years of age. We report an interesting case of a 5 month old female diagnosed with multisystem LCH. Her disease process included osseous, pulmonary, gastrointestinal, cutaneous, hematopoietic and neurologic involvement. This case highlights the varying clinical symptoms, risk factors, pathogenesis, and management of multisystem LCH. This case also emphasizes the role of diagnostic imaging in this multifaceted disease. Elsevier 2021-05-06 /pmc/articles/PMC8120863/ /pubmed/34025890 http://dx.doi.org/10.1016/j.radcr.2021.04.028 Text en © 2021 Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Ji, William
Ladner, Joshua
Rambie, Aimee
Boyer, Kathleen
Multisystem Langerhans Cell Histiocytosis in an infant
title Multisystem Langerhans Cell Histiocytosis in an infant
title_full Multisystem Langerhans Cell Histiocytosis in an infant
title_fullStr Multisystem Langerhans Cell Histiocytosis in an infant
title_full_unstemmed Multisystem Langerhans Cell Histiocytosis in an infant
title_short Multisystem Langerhans Cell Histiocytosis in an infant
title_sort multisystem langerhans cell histiocytosis in an infant
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8120863/
https://www.ncbi.nlm.nih.gov/pubmed/34025890
http://dx.doi.org/10.1016/j.radcr.2021.04.028
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