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Arrhythmogenic Cardiomyopathy Is a Multicellular Disease Affecting Cardiac and Bone Marrow Mesenchymal Stromal Cells

Arrhythmogenic cardiomyopathy (AC) is a familial cardiac disorder at high risk of arrhythmic sudden death in the young and athletes. AC is hallmarked by myocardial replacement with fibro-fatty tissue, favoring life-threatening cardiac arrhythmias and contractile dysfunction. The AC pathogenesis is u...

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Detalles Bibliográficos
Autores principales: Scalco, Arianna, Liboni, Cristina, Angioni, Roberta, Di Bona, Anna, Albiero, Mattia, Bertoldi, Nicole, Fadini, Gian Paolo, Thiene, Gaetano, Chelko, Stephen P., Basso, Cristina, Viola, Antonella, Mongillo, Marco, Zaglia, Tania
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8123444/
https://www.ncbi.nlm.nih.gov/pubmed/33925921
http://dx.doi.org/10.3390/jcm10091871