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Neonatal intrahepatic cholestasis caused by citrin deficiency with no hepatic steatosis: a case report
BACKGROUND: Neonatal intrahepatic cholestasis caused by citrin deficiency (NICCD) is a common form of neonatal jaundice. Histopathological examination of the liver in patients with NICCD typically shows fatty liver, steatohepatitis, and liver fibrosis. Jaundice and fatty liver often improve by 1 yea...
Autores principales: | Miyamoto, Ryosuke, Sada, Jun, Ota, Koki, Kaneko, Kenitiro, Kusano, Hironori, Azuma, Yoshiteru, Okumura, Akihisa |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8130366/ https://www.ncbi.nlm.nih.gov/pubmed/34006251 http://dx.doi.org/10.1186/s12887-021-02717-w |
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