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Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast
Dermatofibrosarcoma protuberans (DFSP) is a soft tissue tumor, usually occurring as a cutaneous lesion localized to the trunk or extremities; although it has a high rate of local recurrence, its metastatic potential is very low and complete surgical excision is frequently curative. Most of the cases...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Pacini Editore srl
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8138493/ https://www.ncbi.nlm.nih.gov/pubmed/31748754 http://dx.doi.org/10.32074/1591-951X-22-19 |
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author | Vecchio, G.M. Broggi, G. Mulè, A. Piombino, E. Magro, G. |
author_facet | Vecchio, G.M. Broggi, G. Mulè, A. Piombino, E. Magro, G. |
author_sort | Vecchio, G.M. |
collection | PubMed |
description | Dermatofibrosarcoma protuberans (DFSP) is a soft tissue tumor, usually occurring as a cutaneous lesion localized to the trunk or extremities; although it has a high rate of local recurrence, its metastatic potential is very low and complete surgical excision is frequently curative. Most of the cases reported as “DFSP of the breast” are tumors arising in the subcutaneous tissue infiltrating the underlying breast parenchyma. To the best of our knowledge, only 5 cases of DFSP of the breast have been reported to date. We herein present a rare case of DFSP of the breast parenchyma in a 41-year-old female with emphasis on the diagnostic clues and the differential diagnosis with other benign and malignant spindle cell lesions of the breast. |
format | Online Article Text |
id | pubmed-8138493 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | Pacini Editore srl |
record_format | MEDLINE/PubMed |
spelling | pubmed-81384932021-07-08 Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast Vecchio, G.M. Broggi, G. Mulè, A. Piombino, E. Magro, G. Pathologica Case Report Dermatofibrosarcoma protuberans (DFSP) is a soft tissue tumor, usually occurring as a cutaneous lesion localized to the trunk or extremities; although it has a high rate of local recurrence, its metastatic potential is very low and complete surgical excision is frequently curative. Most of the cases reported as “DFSP of the breast” are tumors arising in the subcutaneous tissue infiltrating the underlying breast parenchyma. To the best of our knowledge, only 5 cases of DFSP of the breast have been reported to date. We herein present a rare case of DFSP of the breast parenchyma in a 41-year-old female with emphasis on the diagnostic clues and the differential diagnosis with other benign and malignant spindle cell lesions of the breast. Pacini Editore srl 2019-09-01 /pmc/articles/PMC8138493/ /pubmed/31748754 http://dx.doi.org/10.32074/1591-951X-22-19 Text en © 2019 Copyright by Società Italiana di Anatomia Patologica e Citopatologia Diagnostica, Divisione Italiana della International Academy of Pathology https://creativecommons.org/licenses/by-nc-nd/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution NonCommercial-NoDerivatives 4.0 International (CC BY-NC-ND 4.0), which permits for noncommercial use, distribution, and reproduction in any digital medium, provided the original work is properly cited and is not altered in any way. For details, please refer to https://creativecommons.org/licenses/by-nc-nd/4.0/ |
spellingShingle | Case Report Vecchio, G.M. Broggi, G. Mulè, A. Piombino, E. Magro, G. Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
title | Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
title_full | Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
title_fullStr | Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
title_full_unstemmed | Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
title_short | Dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
title_sort | dermatofibrosarcoma protuberans: a tumor in the wide spectrum of the bland-looking spindle cell lesions of the breast |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8138493/ https://www.ncbi.nlm.nih.gov/pubmed/31748754 http://dx.doi.org/10.32074/1591-951X-22-19 |
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