Extracellular Tuning of Mitochondrial Respiration Leads to Aortic Aneurysm

BACKGROUND: Marfan syndrome (MFS) is an autosomal dominant disorder of the connective tissue caused by mutations in the FBN1 (fibrillin-1) gene encoding a large glycoprotein in the extracellular matrix called fibrillin-1. The major complication of this connective disorder is the risk to develop thor...

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Detalles Bibliográficos
Autores principales: Oller, Jorge, Gabandé-Rodríguez, Enrique, Ruiz-Rodríguez, María Jesús, Desdín-Micó, Gabriela, Aranda, Juan Francisco, Rodrigues-Diez, Raquel, Ballesteros-Martínez, Constanza, Blanco, Eva María, Roldan-Montero, Raquel, Acuña, Pedro, Forteza Gil, Alberto, Martín-López, Carlos E., Nistal, J. Francisco, Lino Cardenas, Christian L., Lindsay, Mark Evan, Martín-Ventura, José Luís, Briones, Ana M., Miguel Redondo, Juan, Mittelbrunn, María
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2021
Materias:
Original Research Articles
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8140666/
https://www.ncbi.nlm.nih.gov/pubmed/33709773
http://dx.doi.org/10.1161/CIRCULATIONAHA.120.051171

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