Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor

Potent CFTR modulators improve CF manifestations far beyond expectations, including reduction of risk of typical complications. This is the first report of a patient who developed life-threatening ABPA and emphysema after overwhelming improvement. https://bit.ly/2P96PTy

Detalles Bibliográficos
Autores principales: Mainz, Jochen G., Erdmann, Nina, Duckstein, Franziska, Zagoya, Carlos
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2021
Materias:
Original Research Letters
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8141834/
https://www.ncbi.nlm.nih.gov/pubmed/34046494
http://dx.doi.org/10.1183/23120541.00758-2020
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author Mainz, Jochen G.
Erdmann, Nina
Duckstein, Franziska
Zagoya, Carlos
author_facet Mainz, Jochen G.
Erdmann, Nina
Duckstein, Franziska
Zagoya, Carlos
author_sort Mainz, Jochen G.
collection PubMed
description Potent CFTR modulators improve CF manifestations far beyond expectations, including reduction of risk of typical complications. This is the first report of a patient who developed life-threatening ABPA and emphysema after overwhelming improvement. https://bit.ly/2P96PTy
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spelling pubmed-81418342021-05-26 Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor Mainz, Jochen G. Erdmann, Nina Duckstein, Franziska Zagoya, Carlos ERJ Open Res Original Research Letters Potent CFTR modulators improve CF manifestations far beyond expectations, including reduction of risk of typical complications. This is the first report of a patient who developed life-threatening ABPA and emphysema after overwhelming improvement. https://bit.ly/2P96PTy European Respiratory Society 2021-05-24 /pmc/articles/PMC8141834/ /pubmed/34046494 http://dx.doi.org/10.1183/23120541.00758-2020 Text en Copyright ©The authors 2021 https://creativecommons.org/licenses/by-nc/4.0/This version is distributed under the terms of the Creative Commons Attribution Non-Commercial Licence 4.0. For commercial reproduction rights and permissions contact permissions@ersnet.org (mailto:permissions@ersnet.org)
spellingShingle Original Research Letters
Mainz, Jochen G.
Erdmann, Nina
Duckstein, Franziska
Zagoya, Carlos
Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor
title Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor
title_full Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor
title_fullStr Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor
title_full_unstemmed Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor
title_short Would it have happened without Christmas? Thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the G551D mutation receiving ivacaftor
title_sort would it have happened without christmas? thoracic emphysema and allergic bronchopulmonary aspergillosis in a juvenile cystic fibrosis patient with the g551d mutation receiving ivacaftor
topic Original Research Letters
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8141834/
https://www.ncbi.nlm.nih.gov/pubmed/34046494
http://dx.doi.org/10.1183/23120541.00758-2020
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