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Different Lipid Signature in Fibroblasts of Long-Chain Fatty Acid Oxidation Disorders
Long-chain fatty acid oxidation disorders (lc-FAOD) are a group of diseases affecting the degradation of long-chain fatty acids. In order to investigate the disease specific alterations of the cellular lipidome, we performed undirected lipidomics in fibroblasts from patients with carnitine palmitoyl...
Autores principales: | Alatibi, Khaled I., Hagenbuchner, Judith, Wehbe, Zeinab, Karall, Daniela, Ausserlechner, Michael J., Vockley, Jerry, Spiekerkoetter, Ute, Grünert, Sarah C., Tucci, Sara |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8157847/ https://www.ncbi.nlm.nih.gov/pubmed/34069977 http://dx.doi.org/10.3390/cells10051239 |
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