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Liver Fibrosis and Steatosis in Alström Syndrome: A Genetic Model for Metabolic Syndrome

Alström syndrome (ALMS) is an ultra-rare monogenic disease characterized by insulin resistance, multi-organ fibrosis, obesity, type 2 diabetes mellitus (T2DM), and hypertriglyceridemia with high and early incidence of non-alcoholic fatty liver disease (NAFLD). We evaluated liver fibrosis quantifying...

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Detalles Bibliográficos
Autores principales:	Bettini, Silvia, Bombonato, Giancarlo, Dassie, Francesca, Favaretto, Francesca, Piffer, Luca, Bizzotto, Paola, Busetto, Luca, Chemello, Liliana, Senzolo, Marco, Merkel, Carlo, Angeli, Paolo, Vettor, Roberto, Milan, Gabriella, Maffei, Pietro
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8170882/ https://www.ncbi.nlm.nih.gov/pubmed/33924909 http://dx.doi.org/10.3390/diagnostics11050797

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