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Clinical characteristics, visceral involvement, and mortality in at-risk or early diffuse systemic sclerosis: a longitudinal analysis of an observational prospective multicenter US cohort

BACKGROUND: Early diffuse cutaneous systemic sclerosis (dcSSc) has the highest case fatality among rheumatic diseases. We report baseline characteristics, current immunosuppressive therapies, progression of skin and internal organ involvement, and mortality in a multicenter prospective cohort from t...

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Detalles Bibliográficos
Autores principales: Jaafar, Sara, Lescoat, Alain, Huang, Suiyuan, Gordon, Jessica, Hinchcliff, Monique, Shah, Ami A., Assassi, Shervin, Domsic, Robyn, Bernstein, Elana J., Steen, Virginia, Elliott, Sabrina, Hant, Faye, Castelino, Flavia V., Shanmugam, Victoria K., Correia, Chase, Varga, John, Nagaraja, Vivek, Roofeh, David, Frech, Tracy, Khanna, Dinesh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8201684/
https://www.ncbi.nlm.nih.gov/pubmed/34127049
http://dx.doi.org/10.1186/s13075-021-02548-1