Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male

Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose...

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Detalles Bibliográficos
Autores principales: Zarra, Von Lovel, Demegillo, Kenny Jun, Uyking-Naranjo, May, Domado, Ahmad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Journal of the ASEAN Federation of Endocrine Societies 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8214353/
https://www.ncbi.nlm.nih.gov/pubmed/34177094
http://dx.doi.org/10.15605/jafes.036.01.16
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author Zarra, Von Lovel
Demegillo, Kenny Jun
Uyking-Naranjo, May
Domado, Ahmad
author_facet Zarra, Von Lovel
Demegillo, Kenny Jun
Uyking-Naranjo, May
Domado, Ahmad
author_sort Zarra, Von Lovel
collection PubMed
description Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose into the circulation. We report the case of a 27-year-old Filipino male with presumptive DPS from a recurrent right temporo-zygomatic hemangiopericytoma (HPC). The complexity of DPS requires a multidisciplinary approach. Early screening for metastases from HPC may prevent the undesirable sequelae of the disease process.
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spelling pubmed-82143532021-06-25 Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male Zarra, Von Lovel Demegillo, Kenny Jun Uyking-Naranjo, May Domado, Ahmad J ASEAN Fed Endocr Soc Case Report Doege-Potter syndrome (DPS) is a rare paraneoplastic condition characterized by hypoinsulinemic hypoglycemia from a solitary fibrous tumor. The underlying mechanism is the secretion of a prohormone form of insulin-like growth factor II (IGF-II) by the tumor, which causes decreased release of glucose into the circulation. We report the case of a 27-year-old Filipino male with presumptive DPS from a recurrent right temporo-zygomatic hemangiopericytoma (HPC). The complexity of DPS requires a multidisciplinary approach. Early screening for metastases from HPC may prevent the undesirable sequelae of the disease process. Journal of the ASEAN Federation of Endocrine Societies 2021-05-12 2021 /pmc/articles/PMC8214353/ /pubmed/34177094 http://dx.doi.org/10.15605/jafes.036.01.16 Text en © 2021 Journal of the ASEAN Federation of Endocrine Societies https://creativecommons.org/licenses/by-nc/4.0/This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International.
spellingShingle Case Report
Zarra, Von Lovel
Demegillo, Kenny Jun
Uyking-Naranjo, May
Domado, Ahmad
Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male
title Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male
title_full Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male
title_fullStr Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male
title_full_unstemmed Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male
title_short Doege-Potter Syndrome: A Presumptive Case of Metastatic Hemangiopericytoma with Persistent Hypoglycemia in a 27-Year-Old Male
title_sort doege-potter syndrome: a presumptive case of metastatic hemangiopericytoma with persistent hypoglycemia in a 27-year-old male
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8214353/
https://www.ncbi.nlm.nih.gov/pubmed/34177094
http://dx.doi.org/10.15605/jafes.036.01.16
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