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Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treate...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Journal of the ASEAN Federation of Endocrine Societies
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8214356/ https://www.ncbi.nlm.nih.gov/pubmed/34177092 http://dx.doi.org/10.15605/jafes.036.01.04 |
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author | Wong, Poh Shean Yong, Lit Sin Karim, Nor Afidah Binti Gan, Ee Leng Toh, See Guan Adam, Noor Lita Binti |
author_facet | Wong, Poh Shean Yong, Lit Sin Karim, Nor Afidah Binti Gan, Ee Leng Toh, See Guan Adam, Noor Lita Binti |
author_sort | Wong, Poh Shean |
collection | PubMed |
description | Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass. This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures. |
format | Online Article Text |
id | pubmed-8214356 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2021 |
publisher | Journal of the ASEAN Federation of Endocrine Societies |
record_format | MEDLINE/PubMed |
spelling | pubmed-82143562021-06-25 Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia Wong, Poh Shean Yong, Lit Sin Karim, Nor Afidah Binti Gan, Ee Leng Toh, See Guan Adam, Noor Lita Binti J ASEAN Fed Endocr Soc Case Report Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass. This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures. Journal of the ASEAN Federation of Endocrine Societies 2021-04-17 2021 /pmc/articles/PMC8214356/ /pubmed/34177092 http://dx.doi.org/10.15605/jafes.036.01.04 Text en © 2021 Journal of the ASEAN Federation of Endocrine Societies https://creativecommons.org/licenses/by-nc/4.0/This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International. |
spellingShingle | Case Report Wong, Poh Shean Yong, Lit Sin Karim, Nor Afidah Binti Gan, Ee Leng Toh, See Guan Adam, Noor Lita Binti Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia |
title | Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia |
title_full | Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia |
title_fullStr | Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia |
title_full_unstemmed | Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia |
title_short | Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia |
title_sort | rare presentation of right adrenal mass: extramedullary haematopoiesis in a patient with thalassaemia intermedia |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8214356/ https://www.ncbi.nlm.nih.gov/pubmed/34177092 http://dx.doi.org/10.15605/jafes.036.01.04 |
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