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Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia

Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treate...

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Autores principales: Wong, Poh Shean, Yong, Lit Sin, Karim, Nor Afidah Binti, Gan, Ee Leng, Toh, See Guan, Adam, Noor Lita Binti
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Journal of the ASEAN Federation of Endocrine Societies 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8214356/
https://www.ncbi.nlm.nih.gov/pubmed/34177092
http://dx.doi.org/10.15605/jafes.036.01.04
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author Wong, Poh Shean
Yong, Lit Sin
Karim, Nor Afidah Binti
Gan, Ee Leng
Toh, See Guan
Adam, Noor Lita Binti
author_facet Wong, Poh Shean
Yong, Lit Sin
Karim, Nor Afidah Binti
Gan, Ee Leng
Toh, See Guan
Adam, Noor Lita Binti
author_sort Wong, Poh Shean
collection PubMed
description Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass. This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures.
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spelling pubmed-82143562021-06-25 Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia Wong, Poh Shean Yong, Lit Sin Karim, Nor Afidah Binti Gan, Ee Leng Toh, See Guan Adam, Noor Lita Binti J ASEAN Fed Endocr Soc Case Report Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass. This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures. Journal of the ASEAN Federation of Endocrine Societies 2021-04-17 2021 /pmc/articles/PMC8214356/ /pubmed/34177092 http://dx.doi.org/10.15605/jafes.036.01.04 Text en © 2021 Journal of the ASEAN Federation of Endocrine Societies https://creativecommons.org/licenses/by-nc/4.0/This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International.
spellingShingle Case Report
Wong, Poh Shean
Yong, Lit Sin
Karim, Nor Afidah Binti
Gan, Ee Leng
Toh, See Guan
Adam, Noor Lita Binti
Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
title Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
title_full Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
title_fullStr Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
title_full_unstemmed Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
title_short Rare Presentation of Right Adrenal Mass: Extramedullary Haematopoiesis in a Patient with Thalassaemia Intermedia
title_sort rare presentation of right adrenal mass: extramedullary haematopoiesis in a patient with thalassaemia intermedia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8214356/
https://www.ncbi.nlm.nih.gov/pubmed/34177092
http://dx.doi.org/10.15605/jafes.036.01.04
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