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Poikiloderma With Neutropenia and Mastocytosis: A Case Report and a Review of Dermatological Signs
Poikiloderma with neutropenia (PN) is a very rare genetic disorder mainly characterized by poikiloderma and congenital neutropenia, which explains the recurrence of respiratory infections and risk of developing bronchiectasis. Patients are also prone to develop hematological and skin cancers. Here,...
Autores principales: | Piccolo, Vincenzo, Russo, Teresa, Di Pinto, Daniela, Pota, Elvira, Di Martino, Martina, Piluso, Giulio, Ronchi, Andrea, Argenziano, Giuseppe, Di Brizzi, Eugenia Veronica, Santoro, Claudia |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8222900/ https://www.ncbi.nlm.nih.gov/pubmed/34179048 http://dx.doi.org/10.3389/fmed.2021.680363 |
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